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Transcriptomic Changes Related to Cellular Processes with Particular Emphasis on Cell Activation in Lysosomal Storage Diseases from the Group of Mucopolysaccharidoses

Although mucopolysaccharidoses (MPS), inherited metabolic diseases from the group of lysosomal storage diseases (LSD), are monogenic disorders, recent studies indicated that their molecular mechanisms are complicated. Storage of glycosaminoglycans (GAGs), arising from a deficiency in one of the enzy...

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Detalles Bibliográficos
Autores principales:	Rintz, Estera, Gaffke, Lidia, Podlacha, Magdalena, Brokowska, Joanna, Cyske, Zuzanna, Węgrzyn, Grzegorz, Pierzynowska, Karolina
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	MDPI 2020
Materias:	Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7246638/ https://www.ncbi.nlm.nih.gov/pubmed/32366041 http://dx.doi.org/10.3390/ijms21093194

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