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Annular Pattern of Pustular Vasculitis: A Case Report of Unusual Morphological Presentation

Pustular cutaneous vasculitis is a rare entity. Only handful cases are reported from all over the world. They typically present with painful pustules mainly over dorsum of hands and rarely on lower legs. We report a 50-year female who presented with painful pustules arranged in annular pattern predo...

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Autores principales: Sahu, Kananbala, Sirka, Chandra Sekhar, Pradhan, Swetalina, Rout, Arpita Nibedita, Nayak, Subhasini
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Wolters Kluwer - Medknow 2020
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7247651/
https://www.ncbi.nlm.nih.gov/pubmed/32477987
http://dx.doi.org/10.4103/idoj.IDOJ_100_19
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author Sahu, Kananbala
Sirka, Chandra Sekhar
Pradhan, Swetalina
Rout, Arpita Nibedita
Nayak, Subhasini
author_facet Sahu, Kananbala
Sirka, Chandra Sekhar
Pradhan, Swetalina
Rout, Arpita Nibedita
Nayak, Subhasini
author_sort Sahu, Kananbala
collection PubMed
description Pustular cutaneous vasculitis is a rare entity. Only handful cases are reported from all over the world. They typically present with painful pustules mainly over dorsum of hands and rarely on lower legs. We report a 50-year female who presented with painful pustules arranged in annular pattern predominantly distributed over lower limbs. Laboratory investigation ruled out any systemic associations. Histopathology was suggestive of pustular vasculitis. Final diagnosis of idiopathic pustular vasculitis was made. The patient was successfully treated with oral prednisolone and dapsone without any recurrence on follow up. It is the first report of annular morphological presentation of pustular vasculitis.
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spelling pubmed-72476512020-05-29 Annular Pattern of Pustular Vasculitis: A Case Report of Unusual Morphological Presentation Sahu, Kananbala Sirka, Chandra Sekhar Pradhan, Swetalina Rout, Arpita Nibedita Nayak, Subhasini Indian Dermatol Online J Case Report Pustular cutaneous vasculitis is a rare entity. Only handful cases are reported from all over the world. They typically present with painful pustules mainly over dorsum of hands and rarely on lower legs. We report a 50-year female who presented with painful pustules arranged in annular pattern predominantly distributed over lower limbs. Laboratory investigation ruled out any systemic associations. Histopathology was suggestive of pustular vasculitis. Final diagnosis of idiopathic pustular vasculitis was made. The patient was successfully treated with oral prednisolone and dapsone without any recurrence on follow up. It is the first report of annular morphological presentation of pustular vasculitis. Wolters Kluwer - Medknow 2020-03-09 /pmc/articles/PMC7247651/ /pubmed/32477987 http://dx.doi.org/10.4103/idoj.IDOJ_100_19 Text en Copyright: © 2020 Indian Dermatology Online Journal http://creativecommons.org/licenses/by-nc-sa/4.0 This is an open access journal, and articles are distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 4.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as appropriate credit is given and the new creations are licensed under the identical terms.
spellingShingle Case Report
Sahu, Kananbala
Sirka, Chandra Sekhar
Pradhan, Swetalina
Rout, Arpita Nibedita
Nayak, Subhasini
Annular Pattern of Pustular Vasculitis: A Case Report of Unusual Morphological Presentation
title Annular Pattern of Pustular Vasculitis: A Case Report of Unusual Morphological Presentation
title_full Annular Pattern of Pustular Vasculitis: A Case Report of Unusual Morphological Presentation
title_fullStr Annular Pattern of Pustular Vasculitis: A Case Report of Unusual Morphological Presentation
title_full_unstemmed Annular Pattern of Pustular Vasculitis: A Case Report of Unusual Morphological Presentation
title_short Annular Pattern of Pustular Vasculitis: A Case Report of Unusual Morphological Presentation
title_sort annular pattern of pustular vasculitis: a case report of unusual morphological presentation
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7247651/
https://www.ncbi.nlm.nih.gov/pubmed/32477987
http://dx.doi.org/10.4103/idoj.IDOJ_100_19
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