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Undifferentiated embryonal sarcoma of liver: Paradoxical imaging appearance

Undifferentiated embryonal sarcoma of the liver is a rare entity. It is a malignant primitive mesenchymal tumor seen in the pediatric age group often between 6 to 10 years of age. It involves the right lobe of the liver commonly and is usually asymptomatic. Acute presentation in these cases is secon...

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Autores principales: Thombare, Pranav, Verma, Mitusha, Shah, Kant, Doshi, Hiren, Verma, Gita, Patkar, Deepak
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2020
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7256223/
https://www.ncbi.nlm.nih.gov/pubmed/32489512
http://dx.doi.org/10.1016/j.radcr.2020.05.015
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author Thombare, Pranav
Verma, Mitusha
Shah, Kant
Doshi, Hiren
Verma, Gita
Patkar, Deepak
author_facet Thombare, Pranav
Verma, Mitusha
Shah, Kant
Doshi, Hiren
Verma, Gita
Patkar, Deepak
author_sort Thombare, Pranav
collection PubMed
description Undifferentiated embryonal sarcoma of the liver is a rare entity. It is a malignant primitive mesenchymal tumor seen in the pediatric age group often between 6 to 10 years of age. It involves the right lobe of the liver commonly and is usually asymptomatic. Acute presentation in these cases is secondary to its rupture/ wall dehiscence. Alfa fetoprotein, a tumor marker elevated in most of the hepatic malignant tumors is however normal in undifferentiated embryonal sarcoma. Imaging wise it is a large encapsulated multiseptated lesion. It shows a “paradoxical appearance” with a predominantly solid appearance on ultrasonography and cystic appearance on CT/MRI. This is a peculiar feature that can help in the early diagnosis of this entity. Besides, normal serum alfa fetoprotein levels favor its diagnosis. Hereby we present a case of a 5-year-old female child, presented with complaints of acute onset abdominal pain and distension which on imaging investigation showed a liver mass with typical paradoxical appearance on ultrasonography, CT and MRI as described.
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spelling pubmed-72562232020-06-01 Undifferentiated embryonal sarcoma of liver: Paradoxical imaging appearance Thombare, Pranav Verma, Mitusha Shah, Kant Doshi, Hiren Verma, Gita Patkar, Deepak Radiol Case Rep Gastrointestinal Undifferentiated embryonal sarcoma of the liver is a rare entity. It is a malignant primitive mesenchymal tumor seen in the pediatric age group often between 6 to 10 years of age. It involves the right lobe of the liver commonly and is usually asymptomatic. Acute presentation in these cases is secondary to its rupture/ wall dehiscence. Alfa fetoprotein, a tumor marker elevated in most of the hepatic malignant tumors is however normal in undifferentiated embryonal sarcoma. Imaging wise it is a large encapsulated multiseptated lesion. It shows a “paradoxical appearance” with a predominantly solid appearance on ultrasonography and cystic appearance on CT/MRI. This is a peculiar feature that can help in the early diagnosis of this entity. Besides, normal serum alfa fetoprotein levels favor its diagnosis. Hereby we present a case of a 5-year-old female child, presented with complaints of acute onset abdominal pain and distension which on imaging investigation showed a liver mass with typical paradoxical appearance on ultrasonography, CT and MRI as described. Elsevier 2020-05-21 /pmc/articles/PMC7256223/ /pubmed/32489512 http://dx.doi.org/10.1016/j.radcr.2020.05.015 Text en © 2020 The Authors. Published by Elsevier Inc. on behalf of University of Washington. http://creativecommons.org/licenses/by-nc-nd/4.0/ This is an open access article under the CC BY-NC-ND license (http://creativecommons.org/licenses/by-nc-nd/4.0/).
spellingShingle Gastrointestinal
Thombare, Pranav
Verma, Mitusha
Shah, Kant
Doshi, Hiren
Verma, Gita
Patkar, Deepak
Undifferentiated embryonal sarcoma of liver: Paradoxical imaging appearance
title Undifferentiated embryonal sarcoma of liver: Paradoxical imaging appearance
title_full Undifferentiated embryonal sarcoma of liver: Paradoxical imaging appearance
title_fullStr Undifferentiated embryonal sarcoma of liver: Paradoxical imaging appearance
title_full_unstemmed Undifferentiated embryonal sarcoma of liver: Paradoxical imaging appearance
title_short Undifferentiated embryonal sarcoma of liver: Paradoxical imaging appearance
title_sort undifferentiated embryonal sarcoma of liver: paradoxical imaging appearance
topic Gastrointestinal
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7256223/
https://www.ncbi.nlm.nih.gov/pubmed/32489512
http://dx.doi.org/10.1016/j.radcr.2020.05.015
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