Cargando…
Familial Mediterranean Fever Complicated by a Triad of Adrenal Crisis: Amyloid Goiter and Cardiac Amyloidosis
BACKGROUND: FMF is a common disease in the Mediterranean populations and may be complicated by AA amyloidosis. The coexistence of adrenal and thyroid amyloidosis in AA amyloidosis secondary to familial Mediterranean fever (FMF) is an extremely rare reported condition. We presented a previously unrep...
Autores principales: | , , , , , |
---|---|
Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Hindawi
2020
|
Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7256690/ https://www.ncbi.nlm.nih.gov/pubmed/32518703 http://dx.doi.org/10.1155/2020/7865291 |
_version_ | 1783539966865833984 |
---|---|
author | Abukhalaf, Sadi A. Dandis, Beesan W. Za'tari, Tasnim Amro, Adham M. Alzughayyar, Tareq Z. Rajabi, Yazan A. |
author_facet | Abukhalaf, Sadi A. Dandis, Beesan W. Za'tari, Tasnim Amro, Adham M. Alzughayyar, Tareq Z. Rajabi, Yazan A. |
author_sort | Abukhalaf, Sadi A. |
collection | PubMed |
description | BACKGROUND: FMF is a common disease in the Mediterranean populations and may be complicated by AA amyloidosis. The coexistence of adrenal and thyroid amyloidosis in AA amyloidosis secondary to familial Mediterranean fever (FMF) is an extremely rare reported condition. We presented a previously unreported triad of adrenal, thyroid, and cardiac amyloidosis secondary to FMF. Presentation of Case. We reported a 23-year-old Palestinian male patient presented with hypotension, vomiting, diarrhea, and abdominal pain. The patient was subsequently diagnosed to have an adrenal crisis with both amyloid goiter and cardiac amyloidosis. CONCLUSION: It is crucial to recognize the adrenal crisis in patients with AA amyloidosis secondary to FMF who present similarly to acute FMF inflammatory episodes. The adrenal crisis has high morbidity and mortality, especially if not recognized early in the course of the disease. |
format | Online Article Text |
id | pubmed-7256690 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2020 |
publisher | Hindawi |
record_format | MEDLINE/PubMed |
spelling | pubmed-72566902020-06-08 Familial Mediterranean Fever Complicated by a Triad of Adrenal Crisis: Amyloid Goiter and Cardiac Amyloidosis Abukhalaf, Sadi A. Dandis, Beesan W. Za'tari, Tasnim Amro, Adham M. Alzughayyar, Tareq Z. Rajabi, Yazan A. Case Rep Rheumatol Case Report BACKGROUND: FMF is a common disease in the Mediterranean populations and may be complicated by AA amyloidosis. The coexistence of adrenal and thyroid amyloidosis in AA amyloidosis secondary to familial Mediterranean fever (FMF) is an extremely rare reported condition. We presented a previously unreported triad of adrenal, thyroid, and cardiac amyloidosis secondary to FMF. Presentation of Case. We reported a 23-year-old Palestinian male patient presented with hypotension, vomiting, diarrhea, and abdominal pain. The patient was subsequently diagnosed to have an adrenal crisis with both amyloid goiter and cardiac amyloidosis. CONCLUSION: It is crucial to recognize the adrenal crisis in patients with AA amyloidosis secondary to FMF who present similarly to acute FMF inflammatory episodes. The adrenal crisis has high morbidity and mortality, especially if not recognized early in the course of the disease. Hindawi 2020-05-19 /pmc/articles/PMC7256690/ /pubmed/32518703 http://dx.doi.org/10.1155/2020/7865291 Text en Copyright © 2020 Sadi A. Abukhalaf et al. http://creativecommons.org/licenses/by/4.0/ This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited. |
spellingShingle | Case Report Abukhalaf, Sadi A. Dandis, Beesan W. Za'tari, Tasnim Amro, Adham M. Alzughayyar, Tareq Z. Rajabi, Yazan A. Familial Mediterranean Fever Complicated by a Triad of Adrenal Crisis: Amyloid Goiter and Cardiac Amyloidosis |
title | Familial Mediterranean Fever Complicated by a Triad of Adrenal Crisis: Amyloid Goiter and Cardiac Amyloidosis |
title_full | Familial Mediterranean Fever Complicated by a Triad of Adrenal Crisis: Amyloid Goiter and Cardiac Amyloidosis |
title_fullStr | Familial Mediterranean Fever Complicated by a Triad of Adrenal Crisis: Amyloid Goiter and Cardiac Amyloidosis |
title_full_unstemmed | Familial Mediterranean Fever Complicated by a Triad of Adrenal Crisis: Amyloid Goiter and Cardiac Amyloidosis |
title_short | Familial Mediterranean Fever Complicated by a Triad of Adrenal Crisis: Amyloid Goiter and Cardiac Amyloidosis |
title_sort | familial mediterranean fever complicated by a triad of adrenal crisis: amyloid goiter and cardiac amyloidosis |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7256690/ https://www.ncbi.nlm.nih.gov/pubmed/32518703 http://dx.doi.org/10.1155/2020/7865291 |
work_keys_str_mv | AT abukhalafsadia familialmediterraneanfevercomplicatedbyatriadofadrenalcrisisamyloidgoiterandcardiacamyloidosis AT dandisbeesanw familialmediterraneanfevercomplicatedbyatriadofadrenalcrisisamyloidgoiterandcardiacamyloidosis AT zataritasnim familialmediterraneanfevercomplicatedbyatriadofadrenalcrisisamyloidgoiterandcardiacamyloidosis AT amroadhamm familialmediterraneanfevercomplicatedbyatriadofadrenalcrisisamyloidgoiterandcardiacamyloidosis AT alzughayyartareqz familialmediterraneanfevercomplicatedbyatriadofadrenalcrisisamyloidgoiterandcardiacamyloidosis AT rajabiyazana familialmediterraneanfevercomplicatedbyatriadofadrenalcrisisamyloidgoiterandcardiacamyloidosis |