Cargando…

Conservative management of Cantrell syndrome: a case report

Cantrell syndrome (CS) is defined as congenital combination of five anomalies: defects at the lower part of the sternum, anterior diaphragm, midline supraumbilical abdominal wall, diaphragmatic pericardium and ectopia cordis. Antenatal screening should be performed to make an accurate prenatal diagn...

Descripción completa

Detalles Bibliográficos
Autores principales: Schiavone, Marcella, Pizzol, Damiano, Colangelo, Anna Claudia, Antunes, Mario
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Oxford University Press 2020
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7263755/
https://www.ncbi.nlm.nih.gov/pubmed/32509265
http://dx.doi.org/10.1093/jscr/rjaa100
_version_ 1783540847755657216
author Schiavone, Marcella
Pizzol, Damiano
Colangelo, Anna Claudia
Antunes, Mario
author_facet Schiavone, Marcella
Pizzol, Damiano
Colangelo, Anna Claudia
Antunes, Mario
author_sort Schiavone, Marcella
collection PubMed
description Cantrell syndrome (CS) is defined as congenital combination of five anomalies: defects at the lower part of the sternum, anterior diaphragm, midline supraumbilical abdominal wall, diaphragmatic pericardium and ectopia cordis. Antenatal screening should be performed to make an accurate prenatal diagnosis. The prognosis is usually poor with a high mortality early in life. The gold standard management is surgery but its prognosis remains poor. In many low-income settings prenatal examinations and surgery treatment are not possible. In the present case, we report a not surgery managed baby affected by CS, with good clinical conditions after 5 months.
format Online
Article
Text
id pubmed-7263755
institution National Center for Biotechnology Information
language English
publishDate 2020
publisher Oxford University Press
record_format MEDLINE/PubMed
spelling pubmed-72637552020-06-04 Conservative management of Cantrell syndrome: a case report Schiavone, Marcella Pizzol, Damiano Colangelo, Anna Claudia Antunes, Mario J Surg Case Rep Case Report Cantrell syndrome (CS) is defined as congenital combination of five anomalies: defects at the lower part of the sternum, anterior diaphragm, midline supraumbilical abdominal wall, diaphragmatic pericardium and ectopia cordis. Antenatal screening should be performed to make an accurate prenatal diagnosis. The prognosis is usually poor with a high mortality early in life. The gold standard management is surgery but its prognosis remains poor. In many low-income settings prenatal examinations and surgery treatment are not possible. In the present case, we report a not surgery managed baby affected by CS, with good clinical conditions after 5 months. Oxford University Press 2020-06-01 /pmc/articles/PMC7263755/ /pubmed/32509265 http://dx.doi.org/10.1093/jscr/rjaa100 Text en Published by Oxford University Press and JSCR Publishing Ltd. All rights reserved. © The Author(s) 2020. http://creativecommons.org/licenses/by-nc/4.0/ This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/4.0/), which permits non-commercial re-use, distribution, and reproduction in any medium, provided the original work is properly cited. For commercial re-use, please contact journals.permissions@oup.com
spellingShingle Case Report
Schiavone, Marcella
Pizzol, Damiano
Colangelo, Anna Claudia
Antunes, Mario
Conservative management of Cantrell syndrome: a case report
title Conservative management of Cantrell syndrome: a case report
title_full Conservative management of Cantrell syndrome: a case report
title_fullStr Conservative management of Cantrell syndrome: a case report
title_full_unstemmed Conservative management of Cantrell syndrome: a case report
title_short Conservative management of Cantrell syndrome: a case report
title_sort conservative management of cantrell syndrome: a case report
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7263755/
https://www.ncbi.nlm.nih.gov/pubmed/32509265
http://dx.doi.org/10.1093/jscr/rjaa100
work_keys_str_mv AT schiavonemarcella conservativemanagementofcantrellsyndromeacasereport
AT pizzoldamiano conservativemanagementofcantrellsyndromeacasereport
AT colangeloannaclaudia conservativemanagementofcantrellsyndromeacasereport
AT antunesmario conservativemanagementofcantrellsyndromeacasereport