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Motor axonopathies in a mouse model of Duchenne muscular dystrophy
Duchenne muscular dystrophy (DMD) is a fatal neuromuscular disease caused by deleterious mutations in the DMD gene which encodes the dystrophin protein. Skeletal muscle weakness and eventual muscle degradation due to loss of dystrophin are well-documented pathological hallmarks of DMD. In contrast,...
Autores principales: | Dhindsa, Justin S., McCall, Angela L., Strickland, Laura M., Fusco, Anna F., Kahn, Amanda F., ElMallah, Mai K. |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Nature Publishing Group UK
2020
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7265344/ https://www.ncbi.nlm.nih.gov/pubmed/32488044 http://dx.doi.org/10.1038/s41598-020-65824-1 |
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