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Hashimoto's encephalopathy in association with retinitis pigmentosa – First reported case

Hashimoto's Encephalopathy (HE), also known as steroid responsive encephalopathy associated with autoimmune thyroiditis (SREAT), is a proteiform disorder known for its wide spectrum of presentations from subtle neuropsychiatric manifestations, movement disorders, seizures, stroke-like episodes...

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Autores principales: Ghosh, Ritwik, Chatterjee, Subhankar, Roy, Devlina, Dubey, Souvik, Ray, Biman Kanti
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Wolters Kluwer - Medknow 2020
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7266246/
https://www.ncbi.nlm.nih.gov/pubmed/32509688
http://dx.doi.org/10.4103/jfmpc.jfmpc_1197_19
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author Ghosh, Ritwik
Chatterjee, Subhankar
Roy, Devlina
Dubey, Souvik
Ray, Biman Kanti
author_facet Ghosh, Ritwik
Chatterjee, Subhankar
Roy, Devlina
Dubey, Souvik
Ray, Biman Kanti
author_sort Ghosh, Ritwik
collection PubMed
description Hashimoto's Encephalopathy (HE), also known as steroid responsive encephalopathy associated with autoimmune thyroiditis (SREAT), is a proteiform disorder known for its wide spectrum of presentations from subtle neuropsychiatric manifestations, movement disorders, seizures, stroke-like episodes to coma. Here, we report a case of HE which initially masqueraded as bipolar affective disorder (BPAD) and ultimately progressed to generalized tonic clonic seizures and coma. Although SREAT is characterized by exquisite responsive to steroid, in our case it was unresponsive to pulse methylprednisolone therapy. Rapid recovery was noted with intravenous immunoglobulin (IVIG) therapy. This case was also peculiar for its association with non-sydnromic retinitis pigmetosa (RP). To the best of our knowledge, this was the first reported case of HE which was associated with RP.
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spelling pubmed-72662462020-06-04 Hashimoto's encephalopathy in association with retinitis pigmentosa – First reported case Ghosh, Ritwik Chatterjee, Subhankar Roy, Devlina Dubey, Souvik Ray, Biman Kanti J Family Med Prim Care Case Report Hashimoto's Encephalopathy (HE), also known as steroid responsive encephalopathy associated with autoimmune thyroiditis (SREAT), is a proteiform disorder known for its wide spectrum of presentations from subtle neuropsychiatric manifestations, movement disorders, seizures, stroke-like episodes to coma. Here, we report a case of HE which initially masqueraded as bipolar affective disorder (BPAD) and ultimately progressed to generalized tonic clonic seizures and coma. Although SREAT is characterized by exquisite responsive to steroid, in our case it was unresponsive to pulse methylprednisolone therapy. Rapid recovery was noted with intravenous immunoglobulin (IVIG) therapy. This case was also peculiar for its association with non-sydnromic retinitis pigmetosa (RP). To the best of our knowledge, this was the first reported case of HE which was associated with RP. Wolters Kluwer - Medknow 2020-03-26 /pmc/articles/PMC7266246/ /pubmed/32509688 http://dx.doi.org/10.4103/jfmpc.jfmpc_1197_19 Text en Copyright: © 2020 Journal of Family Medicine and Primary Care http://creativecommons.org/licenses/by-nc-sa/4.0 This is an open access journal, and articles are distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 4.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as appropriate credit is given and the new creations are licensed under the identical terms.
spellingShingle Case Report
Ghosh, Ritwik
Chatterjee, Subhankar
Roy, Devlina
Dubey, Souvik
Ray, Biman Kanti
Hashimoto's encephalopathy in association with retinitis pigmentosa – First reported case
title Hashimoto's encephalopathy in association with retinitis pigmentosa – First reported case
title_full Hashimoto's encephalopathy in association with retinitis pigmentosa – First reported case
title_fullStr Hashimoto's encephalopathy in association with retinitis pigmentosa – First reported case
title_full_unstemmed Hashimoto's encephalopathy in association with retinitis pigmentosa – First reported case
title_short Hashimoto's encephalopathy in association with retinitis pigmentosa – First reported case
title_sort hashimoto's encephalopathy in association with retinitis pigmentosa – first reported case
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7266246/
https://www.ncbi.nlm.nih.gov/pubmed/32509688
http://dx.doi.org/10.4103/jfmpc.jfmpc_1197_19
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