Primary mucinous carcinoma of the skin arising from the upper eyelid: A case report and literature review

Primary mucinous carcinoma of the skin (PMCS) is a rare malignant neoplasm of the sweat glands that has an incidence of 1 per 150,000 population. Because of the lack of typical characteristics, it is often misdiagnosed as an epidermoid cyst, pilomatrixoma, or chalazion before resection, with subsequent enucleation performed unintentionally. We present a case of a 51-year-old patient with PMCS in the upper eyelid that was successfully treated at our hospital. Additionally, we reviewed the literature and discussed the diagnosis, primary and adjuvant therapy, and follow-up procedure.