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Melorheostosis in an Adolescent with Limb Length Discrepancy and Management with Epiphysiodesis with Eight Plates

INTRODUCTION: Melorheostosis is a rare bone dysplasia. It is mainly a radiographic diagnosis with distinct findings of endosteal or periosteal sclerosis along the axis of long bones, resembling the flowing wax. It is usually polyostotic and monomelic. Clinical manifestations are pain, limitation of...

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Autores principales: Laliotis, Nikolaos A, Konstandinidis, Panagiotis, Chrysanthou, Chrysanthos K, Papadopoulou, Lizeta
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Indian Orthopaedic Research Group 2019
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7276626/
https://www.ncbi.nlm.nih.gov/pubmed/32547993
http://dx.doi.org/10.13107/jocr.2019.v09.i05.1508
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author Laliotis, Nikolaos A
Konstandinidis, Panagiotis
Chrysanthou, Chrysanthos K
Papadopoulou, Lizeta
author_facet Laliotis, Nikolaos A
Konstandinidis, Panagiotis
Chrysanthou, Chrysanthos K
Papadopoulou, Lizeta
author_sort Laliotis, Nikolaos A
collection PubMed
description INTRODUCTION: Melorheostosis is a rare bone dysplasia. It is mainly a radiographic diagnosis with distinct findings of endosteal or periosteal sclerosis along the axis of long bones, resembling the flowing wax. It is usually polyostotic and monomelic. Clinical manifestations are pain, limitation of joint movements, deformities, and contractures. Leg length discrepancy may be found, usually the affected limb being shorter. CASE PRESENTATION: We present an adolescent boy, with melorheostosis of the lower limb. The affected limb was longer with equally divided discrepancy of the femur and tibia. There were no another symptoms. After a thorough investigation, we performed epiphysiodesis both medial and lateral of the distal femoral and proximal tibial growth plate, using8eight plates. At the end of the growth, there was almost complete equalization of the length of his lower limbs. CONCLUSION: Melorheostosis may be present with leg length discrepancy leg length discrepancy, with an exception, being that the affected limb is longer. Epiphysiodesis with eight plates is an effective method of limb length equalization.
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spelling pubmed-72766262020-06-15 Melorheostosis in an Adolescent with Limb Length Discrepancy and Management with Epiphysiodesis with Eight Plates Laliotis, Nikolaos A Konstandinidis, Panagiotis Chrysanthou, Chrysanthos K Papadopoulou, Lizeta J Orthop Case Rep Case Report INTRODUCTION: Melorheostosis is a rare bone dysplasia. It is mainly a radiographic diagnosis with distinct findings of endosteal or periosteal sclerosis along the axis of long bones, resembling the flowing wax. It is usually polyostotic and monomelic. Clinical manifestations are pain, limitation of joint movements, deformities, and contractures. Leg length discrepancy may be found, usually the affected limb being shorter. CASE PRESENTATION: We present an adolescent boy, with melorheostosis of the lower limb. The affected limb was longer with equally divided discrepancy of the femur and tibia. There were no another symptoms. After a thorough investigation, we performed epiphysiodesis both medial and lateral of the distal femoral and proximal tibial growth plate, using8eight plates. At the end of the growth, there was almost complete equalization of the length of his lower limbs. CONCLUSION: Melorheostosis may be present with leg length discrepancy leg length discrepancy, with an exception, being that the affected limb is longer. Epiphysiodesis with eight plates is an effective method of limb length equalization. Indian Orthopaedic Research Group 2019 /pmc/articles/PMC7276626/ /pubmed/32547993 http://dx.doi.org/10.13107/jocr.2019.v09.i05.1508 Text en Copyright: © Indian Orthopaedic Research Group http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open-access article distributed under the terms of the Creative Commons Attribution-Noncommercial-Share Alike 3.0 Unported, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Laliotis, Nikolaos A
Konstandinidis, Panagiotis
Chrysanthou, Chrysanthos K
Papadopoulou, Lizeta
Melorheostosis in an Adolescent with Limb Length Discrepancy and Management with Epiphysiodesis with Eight Plates
title Melorheostosis in an Adolescent with Limb Length Discrepancy and Management with Epiphysiodesis with Eight Plates
title_full Melorheostosis in an Adolescent with Limb Length Discrepancy and Management with Epiphysiodesis with Eight Plates
title_fullStr Melorheostosis in an Adolescent with Limb Length Discrepancy and Management with Epiphysiodesis with Eight Plates
title_full_unstemmed Melorheostosis in an Adolescent with Limb Length Discrepancy and Management with Epiphysiodesis with Eight Plates
title_short Melorheostosis in an Adolescent with Limb Length Discrepancy and Management with Epiphysiodesis with Eight Plates
title_sort melorheostosis in an adolescent with limb length discrepancy and management with epiphysiodesis with eight plates
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7276626/
https://www.ncbi.nlm.nih.gov/pubmed/32547993
http://dx.doi.org/10.13107/jocr.2019.v09.i05.1508
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