Cargando…
Melorheostosis in an Adolescent with Limb Length Discrepancy and Management with Epiphysiodesis with Eight Plates
INTRODUCTION: Melorheostosis is a rare bone dysplasia. It is mainly a radiographic diagnosis with distinct findings of endosteal or periosteal sclerosis along the axis of long bones, resembling the flowing wax. It is usually polyostotic and monomelic. Clinical manifestations are pain, limitation of...
Autores principales: | , , , |
---|---|
Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Indian Orthopaedic Research Group
2019
|
Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7276626/ https://www.ncbi.nlm.nih.gov/pubmed/32547993 http://dx.doi.org/10.13107/jocr.2019.v09.i05.1508 |
_version_ | 1783542988694093824 |
---|---|
author | Laliotis, Nikolaos A Konstandinidis, Panagiotis Chrysanthou, Chrysanthos K Papadopoulou, Lizeta |
author_facet | Laliotis, Nikolaos A Konstandinidis, Panagiotis Chrysanthou, Chrysanthos K Papadopoulou, Lizeta |
author_sort | Laliotis, Nikolaos A |
collection | PubMed |
description | INTRODUCTION: Melorheostosis is a rare bone dysplasia. It is mainly a radiographic diagnosis with distinct findings of endosteal or periosteal sclerosis along the axis of long bones, resembling the flowing wax. It is usually polyostotic and monomelic. Clinical manifestations are pain, limitation of joint movements, deformities, and contractures. Leg length discrepancy may be found, usually the affected limb being shorter. CASE PRESENTATION: We present an adolescent boy, with melorheostosis of the lower limb. The affected limb was longer with equally divided discrepancy of the femur and tibia. There were no another symptoms. After a thorough investigation, we performed epiphysiodesis both medial and lateral of the distal femoral and proximal tibial growth plate, using8eight plates. At the end of the growth, there was almost complete equalization of the length of his lower limbs. CONCLUSION: Melorheostosis may be present with leg length discrepancy leg length discrepancy, with an exception, being that the affected limb is longer. Epiphysiodesis with eight plates is an effective method of limb length equalization. |
format | Online Article Text |
id | pubmed-7276626 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2019 |
publisher | Indian Orthopaedic Research Group |
record_format | MEDLINE/PubMed |
spelling | pubmed-72766262020-06-15 Melorheostosis in an Adolescent with Limb Length Discrepancy and Management with Epiphysiodesis with Eight Plates Laliotis, Nikolaos A Konstandinidis, Panagiotis Chrysanthou, Chrysanthos K Papadopoulou, Lizeta J Orthop Case Rep Case Report INTRODUCTION: Melorheostosis is a rare bone dysplasia. It is mainly a radiographic diagnosis with distinct findings of endosteal or periosteal sclerosis along the axis of long bones, resembling the flowing wax. It is usually polyostotic and monomelic. Clinical manifestations are pain, limitation of joint movements, deformities, and contractures. Leg length discrepancy may be found, usually the affected limb being shorter. CASE PRESENTATION: We present an adolescent boy, with melorheostosis of the lower limb. The affected limb was longer with equally divided discrepancy of the femur and tibia. There were no another symptoms. After a thorough investigation, we performed epiphysiodesis both medial and lateral of the distal femoral and proximal tibial growth plate, using8eight plates. At the end of the growth, there was almost complete equalization of the length of his lower limbs. CONCLUSION: Melorheostosis may be present with leg length discrepancy leg length discrepancy, with an exception, being that the affected limb is longer. Epiphysiodesis with eight plates is an effective method of limb length equalization. Indian Orthopaedic Research Group 2019 /pmc/articles/PMC7276626/ /pubmed/32547993 http://dx.doi.org/10.13107/jocr.2019.v09.i05.1508 Text en Copyright: © Indian Orthopaedic Research Group http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open-access article distributed under the terms of the Creative Commons Attribution-Noncommercial-Share Alike 3.0 Unported, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited. |
spellingShingle | Case Report Laliotis, Nikolaos A Konstandinidis, Panagiotis Chrysanthou, Chrysanthos K Papadopoulou, Lizeta Melorheostosis in an Adolescent with Limb Length Discrepancy and Management with Epiphysiodesis with Eight Plates |
title | Melorheostosis in an Adolescent with Limb Length Discrepancy and Management with Epiphysiodesis with Eight Plates |
title_full | Melorheostosis in an Adolescent with Limb Length Discrepancy and Management with Epiphysiodesis with Eight Plates |
title_fullStr | Melorheostosis in an Adolescent with Limb Length Discrepancy and Management with Epiphysiodesis with Eight Plates |
title_full_unstemmed | Melorheostosis in an Adolescent with Limb Length Discrepancy and Management with Epiphysiodesis with Eight Plates |
title_short | Melorheostosis in an Adolescent with Limb Length Discrepancy and Management with Epiphysiodesis with Eight Plates |
title_sort | melorheostosis in an adolescent with limb length discrepancy and management with epiphysiodesis with eight plates |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7276626/ https://www.ncbi.nlm.nih.gov/pubmed/32547993 http://dx.doi.org/10.13107/jocr.2019.v09.i05.1508 |
work_keys_str_mv | AT laliotisnikolaosa melorheostosisinanadolescentwithlimblengthdiscrepancyandmanagementwithepiphysiodesiswitheightplates AT konstandinidispanagiotis melorheostosisinanadolescentwithlimblengthdiscrepancyandmanagementwithepiphysiodesiswitheightplates AT chrysanthouchrysanthosk melorheostosisinanadolescentwithlimblengthdiscrepancyandmanagementwithepiphysiodesiswitheightplates AT papadopouloulizeta melorheostosisinanadolescentwithlimblengthdiscrepancyandmanagementwithepiphysiodesiswitheightplates |