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Pathophysiology of Hip Disorders in Patients with Mucopolysaccharidosis IVA

Patients with mucopolysaccharidoses IVA (MPS IVA) have a progressive accumulation of the specific glycosaminoglycans (GAGs): chondroitin-6-sulfate (C6S) and keratan sulfate (KS), leading to the degeneration of the cartilage matrix and its connective tissue perturbing the regular microarchitecture of...

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Detalles Bibliográficos
Autores principales:	Wang, Zhigang, Xu, Yunlan, Jiang, Enze, Wang, Jianmin, Tomatsu, Shunji, Shen, Kaiying
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	MDPI 2020
Materias:	Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7277472/ https://www.ncbi.nlm.nih.gov/pubmed/32365519 http://dx.doi.org/10.3390/diagnostics10050264

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