Primary Adrenal Leiomyosarcoma: Clinical, Radiological, and Histopathological Characteristics

Primary adrenal leiomyosarcoma (PAL) is a rare, high-grade proliferating mesenchymal tumor with a considerable risk of metastasis, deriving from the smooth muscle wall of a central adrenal vein, or its tributaries. Roughly 40 patients with PAL have been reported in the literature. Herein, we present...

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Autores principales: Jabarkhel, Fatema, Puttonen, Henri, Hansson, Lina, Muth, Andreas, Ragnarsson, Oskar
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Oxford University Press 2020
Materias:
Case Reports
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7278282/
https://www.ncbi.nlm.nih.gov/pubmed/32537544
http://dx.doi.org/10.1210/jendso/bvaa055
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author Jabarkhel, Fatema
Puttonen, Henri
Hansson, Lina
Muth, Andreas
Ragnarsson, Oskar
author_facet Jabarkhel, Fatema
Puttonen, Henri
Hansson, Lina
Muth, Andreas
Ragnarsson, Oskar
author_sort Jabarkhel, Fatema
collection PubMed
description Primary adrenal leiomyosarcoma (PAL) is a rare, high-grade proliferating mesenchymal tumor with a considerable risk of metastasis, deriving from the smooth muscle wall of a central adrenal vein, or its tributaries. Roughly 40 patients with PAL have been reported in the literature. Herein, we present 3 patients with incidentally discovered PAL, along with an overview of the current knowledge on the clinical, radiological, and histopathological characteristics of PAL.
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spelling pubmed-72782822020-06-12 Primary Adrenal Leiomyosarcoma: Clinical, Radiological, and Histopathological Characteristics Jabarkhel, Fatema Puttonen, Henri Hansson, Lina Muth, Andreas Ragnarsson, Oskar J Endocr Soc Case Reports Primary adrenal leiomyosarcoma (PAL) is a rare, high-grade proliferating mesenchymal tumor with a considerable risk of metastasis, deriving from the smooth muscle wall of a central adrenal vein, or its tributaries. Roughly 40 patients with PAL have been reported in the literature. Herein, we present 3 patients with incidentally discovered PAL, along with an overview of the current knowledge on the clinical, radiological, and histopathological characteristics of PAL. Oxford University Press 2020-05-15 /pmc/articles/PMC7278282/ /pubmed/32537544 http://dx.doi.org/10.1210/jendso/bvaa055 Text en © Endocrine Society 2020. http://creativecommons.org/licenses/by-nc-nd/4.0/ This is an Open Access article distributed under the terms of the Creative Commons Attribution-NonCommercial-NoDerivs licence (http://creativecommons.org/licenses/by-nc-nd/4.0/), which permits non-commercial reproduction and distribution of the work, in any medium, provided the original work is not altered or transformed in any way, and that the work is properly cited. For commercial re-use, please contact journals.permissions@oup.com
spellingShingle Case Reports
Jabarkhel, Fatema
Puttonen, Henri
Hansson, Lina
Muth, Andreas
Ragnarsson, Oskar
Primary Adrenal Leiomyosarcoma: Clinical, Radiological, and Histopathological Characteristics
title Primary Adrenal Leiomyosarcoma: Clinical, Radiological, and Histopathological Characteristics
title_full Primary Adrenal Leiomyosarcoma: Clinical, Radiological, and Histopathological Characteristics
title_fullStr Primary Adrenal Leiomyosarcoma: Clinical, Radiological, and Histopathological Characteristics
title_full_unstemmed Primary Adrenal Leiomyosarcoma: Clinical, Radiological, and Histopathological Characteristics
title_short Primary Adrenal Leiomyosarcoma: Clinical, Radiological, and Histopathological Characteristics
title_sort primary adrenal leiomyosarcoma: clinical, radiological, and histopathological characteristics
topic Case Reports
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7278282/
https://www.ncbi.nlm.nih.gov/pubmed/32537544
http://dx.doi.org/10.1210/jendso/bvaa055
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