Aortic Valve–Sparing Surgical Treatment of Supravalvar Aortic Stenosis in a 65-Year-Old Adult

Supravalvar aortic stenosis (SVAS) is a rare congenital cardiac disease that usually co-occurs with Williams syndrome. In the adult population, a few SVAS cases have been reported in patients affected by homozygous familial hypercholesterolemia. However, because of the rarity of this disease entity,...

Descripción completa

Detalles Bibliográficos
Autores principales: Shin, Hong Ju, Shin, Jae Seung
Formato: Online Artículo Texto
Lenguaje:English
Publicado: The Korean Society for Thoracic and Cardiovascular Surgery 2020
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7287217/
https://www.ncbi.nlm.nih.gov/pubmed/32551296
http://dx.doi.org/10.5090/kjtcs.2020.53.3.144
Descripción
Sumario:Supravalvar aortic stenosis (SVAS) is a rare congenital cardiac disease that usually co-occurs with Williams syndrome. In the adult population, a few SVAS cases have been reported in patients affected by homozygous familial hypercholesterolemia. However, because of the rarity of this disease entity, there is no standard surgical treatment for SVAS. Here, we present a case of successful surgical treatment using an autologous excised aortic patch in a 65-year-old patient with SVAS.

Ejemplares similares