Aortic Valve–Sparing Surgical Treatment of Supravalvar Aortic Stenosis in a 65-Year-Old Adult

Supravalvar aortic stenosis (SVAS) is a rare congenital cardiac disease that usually co-occurs with Williams syndrome. In the adult population, a few SVAS cases have been reported in patients affected by homozygous familial hypercholesterolemia. However, because of the rarity of this disease entity,...

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Detalles Bibliográficos
Autores principales: Shin, Hong Ju, Shin, Jae Seung
Formato: Online Artículo Texto
Lenguaje:English
Publicado: The Korean Society for Thoracic and Cardiovascular Surgery 2020
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7287217/
https://www.ncbi.nlm.nih.gov/pubmed/32551296
http://dx.doi.org/10.5090/kjtcs.2020.53.3.144
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author Shin, Hong Ju
Shin, Jae Seung
author_facet Shin, Hong Ju
Shin, Jae Seung
author_sort Shin, Hong Ju
collection PubMed
description Supravalvar aortic stenosis (SVAS) is a rare congenital cardiac disease that usually co-occurs with Williams syndrome. In the adult population, a few SVAS cases have been reported in patients affected by homozygous familial hypercholesterolemia. However, because of the rarity of this disease entity, there is no standard surgical treatment for SVAS. Here, we present a case of successful surgical treatment using an autologous excised aortic patch in a 65-year-old patient with SVAS.
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spelling pubmed-72872172020-06-17 Aortic Valve–Sparing Surgical Treatment of Supravalvar Aortic Stenosis in a 65-Year-Old Adult Shin, Hong Ju Shin, Jae Seung Korean J Thorac Cardiovasc Surg Case Report Supravalvar aortic stenosis (SVAS) is a rare congenital cardiac disease that usually co-occurs with Williams syndrome. In the adult population, a few SVAS cases have been reported in patients affected by homozygous familial hypercholesterolemia. However, because of the rarity of this disease entity, there is no standard surgical treatment for SVAS. Here, we present a case of successful surgical treatment using an autologous excised aortic patch in a 65-year-old patient with SVAS. The Korean Society for Thoracic and Cardiovascular Surgery 2020-06-05 2020-06-05 /pmc/articles/PMC7287217/ /pubmed/32551296 http://dx.doi.org/10.5090/kjtcs.2020.53.3.144 Text en Copyright © The Korean Society for Thoracic and Cardiovascular Surgery. 2020. All right reserved. This is an open-access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/4.0) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Shin, Hong Ju
Shin, Jae Seung
Aortic Valve–Sparing Surgical Treatment of Supravalvar Aortic Stenosis in a 65-Year-Old Adult
title Aortic Valve–Sparing Surgical Treatment of Supravalvar Aortic Stenosis in a 65-Year-Old Adult
title_full Aortic Valve–Sparing Surgical Treatment of Supravalvar Aortic Stenosis in a 65-Year-Old Adult
title_fullStr Aortic Valve–Sparing Surgical Treatment of Supravalvar Aortic Stenosis in a 65-Year-Old Adult
title_full_unstemmed Aortic Valve–Sparing Surgical Treatment of Supravalvar Aortic Stenosis in a 65-Year-Old Adult
title_short Aortic Valve–Sparing Surgical Treatment of Supravalvar Aortic Stenosis in a 65-Year-Old Adult
title_sort aortic valve–sparing surgical treatment of supravalvar aortic stenosis in a 65-year-old adult
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7287217/
https://www.ncbi.nlm.nih.gov/pubmed/32551296
http://dx.doi.org/10.5090/kjtcs.2020.53.3.144
work_keys_str_mv AT shinhongju aorticvalvesparingsurgicaltreatmentofsupravalvaraorticstenosisina65yearoldadult
AT shinjaeseung aorticvalvesparingsurgicaltreatmentofsupravalvaraorticstenosisina65yearoldadult

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