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Relationship of CT densitometry to lung physiological parameters and health status in alpha-1 antitrypsin deficiency: initial report of a centralised database of the NIHR rare diseases translational research collaborative

OBJECTIVES: To establish a database network for the study of alpha-1 antitrypsin deficiency (AATD) and compare the results to CT lung density as the most direct measure of emphysema. DESIGN: A central electronic database was established to permit the upload of anonymised patient data from remote sit...

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Detalles Bibliográficos
Autores principales:	Crossley, Diana, Stockley, James, Bolton, Charlotte E, Hopkinson, Nicholas S, Mahadeva, Ravi, Steiner, Michael, Wilkinson, Tom, Hurst, John R, Gooptu, Bibek, Stockley, Robert A
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	BMJ Publishing Group 2020
Materias:	Respiratory Medicine
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7328802/ https://www.ncbi.nlm.nih.gov/pubmed/32606060 http://dx.doi.org/10.1136/bmjopen-2019-036045

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