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N-Acetylcysteine Reduces Skeletal Muscles Oxidative Stress and Improves Grip Strength in Dysferlin-Deficient Bla/J Mice
Dysferlinopathy is an autosomal recessive muscular dystrophy resulting from mutations in the dysferlin gene. Absence of dysferlin in the sarcolemma and progressive muscle wasting are hallmarks of this disease. Signs of oxidative stress have been observed in skeletal muscles of dysferlinopathy patien...
Autores principales: | García-Campos, Paz, Báez-Matus, Ximena, Jara-Gutiérrez, Carlos, Paz-Araos, Marilyn, Astorga, César, Cea, Luis A., Rodríguez, Viviana, Bevilacqua, Jorge A., Caviedes, Pablo, Cárdenas, Ana M. |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
MDPI
2020
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7352960/ https://www.ncbi.nlm.nih.gov/pubmed/32560255 http://dx.doi.org/10.3390/ijms21124293 |
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