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Klippel–Trenaunay Syndrome with Arterio-veno-lymphatic Malformation: A Rare Presentation

Klippel–Trenaunay syndrome (KTS) is a rare disorder characterized by triad of vascular malformations, varicose veins, and bony or soft tissue hypertrophy involving an extremity. Port wine stain is the most common vascular malformation associated with this syndrome. Various other rare vascular malfor...

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Detalles Bibliográficos
Autores principales: Supekar, Bhagyashree B., Chopkar, Apoorva D., Wankhade, Vaishali H., Singh, Rajesh Pratap, Bhat, Dharitri Mukund, Suresh, Parvathy
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Wolters Kluwer - Medknow 2020
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7367591/
https://www.ncbi.nlm.nih.gov/pubmed/32695703
http://dx.doi.org/10.4103/idoj.IDOJ_220_19
Descripción
Sumario:Klippel–Trenaunay syndrome (KTS) is a rare disorder characterized by triad of vascular malformations, varicose veins, and bony or soft tissue hypertrophy involving an extremity. Port wine stain is the most common vascular malformation associated with this syndrome. Various other rare vascular malformations described are angiokeratomas, angiokeratoma circumscriptum naeviformae, angiodermatitis, etc. This is the first instance, to the best of our knowledge, describing the capillary, venous, and lymphatic malformations in a same case of KTS.