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Murine type VII collagen distorts outcome in human skin graft mouse model for dystrophic epidermolysis bullosa
Human skin graft mouse models are widely used to investigate and develop therapeutic strategies for the severe generalized form of recessive dystrophic epidermolysis bullosa (RDEB), which is caused by biallelic null mutations in COL7A1 and the complete absence of type VII collagen (C7). Most therape...
Autores principales: | Bremer, Jeroen, Kramer, Duco, Eichhorn, Daryll S., Gostyński, Antoni, Diercks, Gilles F. H., Jonkman, Marcel F., van den Akker, Peter C., Pasmooij, Anna M. G. |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
John Wiley and Sons Inc.
2018
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7380020/ https://www.ncbi.nlm.nih.gov/pubmed/30019435 http://dx.doi.org/10.1111/exd.13744 |
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