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Nutritional ketosis improves exercise metabolism in patients with very long‐chain acyl‐CoA dehydrogenase deficiency

A maladaptive shift from fat to carbohydrate (CHO) oxidation during exercise is thought to underlie myopathy and exercise‐induced rhabdomyolysis in patients with fatty acid oxidation (FAO) disorders. We hypothesised that ingestion of a ketone ester (KE) drink prior to exercise could serve as an alte...

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Detalles Bibliográficos
Autores principales:	Bleeker, Jeannette C., Visser, Gepke, Clarke, Kieran, Ferdinandusse, Sacha, de Haan, Ferdinand H., Houtkooper, Riekelt H., IJlst, Lodewijk, Kok, Irene L., Langeveld, Mirjam, van der Pol, W. Ludo, de Sain‐van der Velden, Monique G. M., Sibeijn‐Kuiper, Anita, Takken, Tim, Wanders, Ronald J. A., van Weeghel, Michel, Wijburg, Frits A., van der Woude, Luc H., Wüst, Rob C. I., Cox, Pete J., Jeneson, Jeroen A. L.
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	John Wiley & Sons, Inc. 2020
Materias:	Original Articles
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7384182/ https://www.ncbi.nlm.nih.gov/pubmed/31955429 http://dx.doi.org/10.1002/jimd.12217

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