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Vaginal Reconstruction in Patients with Mayer–Rokitansky–Küster–Hauser Syndrome—One Centre Experience

Background and Objectives: The Mayer–Rokitansky–Küster–Hauser syndrome is a congenital condition in which patients are born with vaginal and uterus agenesis, affecting the ability to have a normal sexual life and to bear children. Vaginal reconstruction is a challenging procedure for plastic surgeon...

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Autores principales: Avino, Adelaida, Răducu, Laura, Tulin, Adrian, Gheoca-Mutu, Daniela-Elena, Balcangiu-Stroescu, Andra-Elena, Marina, Cristina-Nicoleta, Jecan, Cristian-Radu
Formato: Online Artículo Texto
Lenguaje:English
Publicado: MDPI 2020
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7404697/
https://www.ncbi.nlm.nih.gov/pubmed/32630225
http://dx.doi.org/10.3390/medicina56070327
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author Avino, Adelaida
Răducu, Laura
Tulin, Adrian
Gheoca-Mutu, Daniela-Elena
Balcangiu-Stroescu, Andra-Elena
Marina, Cristina-Nicoleta
Jecan, Cristian-Radu
author_facet Avino, Adelaida
Răducu, Laura
Tulin, Adrian
Gheoca-Mutu, Daniela-Elena
Balcangiu-Stroescu, Andra-Elena
Marina, Cristina-Nicoleta
Jecan, Cristian-Radu
author_sort Avino, Adelaida
collection PubMed
description Background and Objectives: The Mayer–Rokitansky–Küster–Hauser syndrome is a congenital condition in which patients are born with vaginal and uterus agenesis, affecting the ability to have a normal sexual life and to bear children. Vaginal reconstruction is a challenging procedure for plastic surgeons. The aim of this study is to report our experience in the management of twelve patients with congenital absence of the vagina due to the MRKH syndrome. Materials and Methods: We performed a retrospective study on 12 patients admitted to the Plastic Surgery Department of the Clinical Emergency Hospital “Prof. Dr. Agrippa Ionescu”, Bucharest, Romania, for vaginal reconstruction within a period of eleven years (January 2009–December 2019). All patients were diagnosed by the gynaecologists with vaginal agenesis, as part of the Mayer–Rokitansky–Küster–Hauser syndrome. The Abbe‘–McIndoe technique with an autologous skin graft was performed in all cases. Results: The average age of our patients was 20.16 (16–28) years. All patients were 46 XX. The average surgical timing was 3.05 h (range 2.85–4h). Postoperative rectovaginal fistula was encountered in 1 patient. Postoperative average vaginal length was 10.4 cm (range 9.8–12.1 cm). Regular sexual life was achieved in 10 patients. Conclusion: Nowadays, there is no established standard method of vaginal reconstruction. In Romania, the McIndoe technique is the most applied. Unfortunately, even if the MRKH syndrome is not uncommon, less and less surgeons are willing to perform the procedure to create a neovagina.
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spelling pubmed-74046972020-08-11 Vaginal Reconstruction in Patients with Mayer–Rokitansky–Küster–Hauser Syndrome—One Centre Experience Avino, Adelaida Răducu, Laura Tulin, Adrian Gheoca-Mutu, Daniela-Elena Balcangiu-Stroescu, Andra-Elena Marina, Cristina-Nicoleta Jecan, Cristian-Radu Medicina (Kaunas) Article Background and Objectives: The Mayer–Rokitansky–Küster–Hauser syndrome is a congenital condition in which patients are born with vaginal and uterus agenesis, affecting the ability to have a normal sexual life and to bear children. Vaginal reconstruction is a challenging procedure for plastic surgeons. The aim of this study is to report our experience in the management of twelve patients with congenital absence of the vagina due to the MRKH syndrome. Materials and Methods: We performed a retrospective study on 12 patients admitted to the Plastic Surgery Department of the Clinical Emergency Hospital “Prof. Dr. Agrippa Ionescu”, Bucharest, Romania, for vaginal reconstruction within a period of eleven years (January 2009–December 2019). All patients were diagnosed by the gynaecologists with vaginal agenesis, as part of the Mayer–Rokitansky–Küster–Hauser syndrome. The Abbe‘–McIndoe technique with an autologous skin graft was performed in all cases. Results: The average age of our patients was 20.16 (16–28) years. All patients were 46 XX. The average surgical timing was 3.05 h (range 2.85–4h). Postoperative rectovaginal fistula was encountered in 1 patient. Postoperative average vaginal length was 10.4 cm (range 9.8–12.1 cm). Regular sexual life was achieved in 10 patients. Conclusion: Nowadays, there is no established standard method of vaginal reconstruction. In Romania, the McIndoe technique is the most applied. Unfortunately, even if the MRKH syndrome is not uncommon, less and less surgeons are willing to perform the procedure to create a neovagina. MDPI 2020-07-01 /pmc/articles/PMC7404697/ /pubmed/32630225 http://dx.doi.org/10.3390/medicina56070327 Text en © 2020 by the authors. Licensee MDPI, Basel, Switzerland. This article is an open access article distributed under the terms and conditions of the Creative Commons Attribution (CC BY) license (http://creativecommons.org/licenses/by/4.0/).
spellingShingle Article
Avino, Adelaida
Răducu, Laura
Tulin, Adrian
Gheoca-Mutu, Daniela-Elena
Balcangiu-Stroescu, Andra-Elena
Marina, Cristina-Nicoleta
Jecan, Cristian-Radu
Vaginal Reconstruction in Patients with Mayer–Rokitansky–Küster–Hauser Syndrome—One Centre Experience
title Vaginal Reconstruction in Patients with Mayer–Rokitansky–Küster–Hauser Syndrome—One Centre Experience
title_full Vaginal Reconstruction in Patients with Mayer–Rokitansky–Küster–Hauser Syndrome—One Centre Experience
title_fullStr Vaginal Reconstruction in Patients with Mayer–Rokitansky–Küster–Hauser Syndrome—One Centre Experience
title_full_unstemmed Vaginal Reconstruction in Patients with Mayer–Rokitansky–Küster–Hauser Syndrome—One Centre Experience
title_short Vaginal Reconstruction in Patients with Mayer–Rokitansky–Küster–Hauser Syndrome—One Centre Experience
title_sort vaginal reconstruction in patients with mayer–rokitansky–küster–hauser syndrome—one centre experience
topic Article
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7404697/
https://www.ncbi.nlm.nih.gov/pubmed/32630225
http://dx.doi.org/10.3390/medicina56070327
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