Sclerosing epithelioid fibrosarcoma: rare and serious

Sclerosing Epithelioid Fibrosarcoma (SEF) is a rare form of soft tissue sarcoma. It is characterized by a slow evolution, with local recurrences and late metastases that are mainly pulmonary and pleural in about 50% of cases. The treatment is based on the surgery which must be as wide as possible. T...

Descripción completa

Detalles Bibliográficos
Autores principales: Yahyaoui, Mounir, Benhammou, Mohammed, Aharram, Soufiane, Amghar, Jawad, Sadougui, Mohammed, Agoumi, Omar, Daoudi, Abdelkrim
Formato: Online Artículo Texto
Lenguaje:English
Publicado: The African Field Epidemiology Network 2020
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7422754/
https://www.ncbi.nlm.nih.gov/pubmed/32849986
http://dx.doi.org/10.11604/pamj.2020.36.131.18668
Descripción
Sumario:Sclerosing Epithelioid Fibrosarcoma (SEF) is a rare form of soft tissue sarcoma. It is characterized by a slow evolution, with local recurrences and late metastases that are mainly pulmonary and pleural in about 50% of cases. The treatment is based on the surgery which must be as wide as possible. The efficacy of adjuvant therapy in the control of SEF is not yet demonstrated. Chemotherapy is used in recurrences, some have also proposed radiotherapy. Long-term follow-up of patients with SEF is therefore essential.

Ejemplares similares