Epithelioid malignant peripheral nerve sheath tumor arising in schwannoma

Epithelioid malignant peripheral nerve sheath tumor (EMPNST, malignant epithelioid schwannoma) is a rare variant of malignant peripheral nerve sheath tumor that has morphologic and immunophenotypic overlap with a variety of epithelioid neoplasms. Because of its rarity it may be potentially underreco...

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Autores principales: Heatley, Nicholas, Kolson Kokohaare, Eva, Strauss, Dirk C, Hallin, Magnus, Jones, Robin L, Fisher, Cyril, Thway, Khin
Formato: Online Artículo Texto
Lenguaje:English
Publicado: SAGE Publications 2020
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7443986/
https://www.ncbi.nlm.nih.gov/pubmed/32913618
http://dx.doi.org/10.1177/2036361320950862
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author Heatley, Nicholas
Kolson Kokohaare, Eva
Strauss, Dirk C
Hallin, Magnus
Jones, Robin L
Fisher, Cyril
Thway, Khin
author_facet Heatley, Nicholas
Kolson Kokohaare, Eva
Strauss, Dirk C
Hallin, Magnus
Jones, Robin L
Fisher, Cyril
Thway, Khin
author_sort Heatley, Nicholas
collection PubMed
description Epithelioid malignant peripheral nerve sheath tumor (EMPNST, malignant epithelioid schwannoma) is a rare variant of malignant peripheral nerve sheath tumor that has morphologic and immunophenotypic overlap with a variety of epithelioid neoplasms. Because of its rarity it may be potentially underrecognized. We describe a case arising in the subcutis of the thigh in a 25 year-old female, and discuss the pathologic features and differential diagnosis.
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spelling pubmed-74439862020-09-09 Epithelioid malignant peripheral nerve sheath tumor arising in schwannoma Heatley, Nicholas Kolson Kokohaare, Eva Strauss, Dirk C Hallin, Magnus Jones, Robin L Fisher, Cyril Thway, Khin Rare Tumors Case Report Epithelioid malignant peripheral nerve sheath tumor (EMPNST, malignant epithelioid schwannoma) is a rare variant of malignant peripheral nerve sheath tumor that has morphologic and immunophenotypic overlap with a variety of epithelioid neoplasms. Because of its rarity it may be potentially underrecognized. We describe a case arising in the subcutis of the thigh in a 25 year-old female, and discuss the pathologic features and differential diagnosis. SAGE Publications 2020-08-21 /pmc/articles/PMC7443986/ /pubmed/32913618 http://dx.doi.org/10.1177/2036361320950862 Text en © The Author(s) 2020 https://creativecommons.org/licenses/by-nc/4.0/ This article is distributed under the terms of the Creative Commons Attribution-NonCommercial 4.0 License (https://creativecommons.org/licenses/by-nc/4.0/) which permits non-commercial use, reproduction and distribution of the work without further permission provided the original work is attributed as specified on the SAGE and Open Access pages (https://us.sagepub.com/en-us/nam/open-access-at-sage).
spellingShingle Case Report
Heatley, Nicholas
Kolson Kokohaare, Eva
Strauss, Dirk C
Hallin, Magnus
Jones, Robin L
Fisher, Cyril
Thway, Khin
Epithelioid malignant peripheral nerve sheath tumor arising in schwannoma
title Epithelioid malignant peripheral nerve sheath tumor arising in schwannoma
title_full Epithelioid malignant peripheral nerve sheath tumor arising in schwannoma
title_fullStr Epithelioid malignant peripheral nerve sheath tumor arising in schwannoma
title_full_unstemmed Epithelioid malignant peripheral nerve sheath tumor arising in schwannoma
title_short Epithelioid malignant peripheral nerve sheath tumor arising in schwannoma
title_sort epithelioid malignant peripheral nerve sheath tumor arising in schwannoma
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7443986/
https://www.ncbi.nlm.nih.gov/pubmed/32913618
http://dx.doi.org/10.1177/2036361320950862
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