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Mechanisms of Mitochondrial Dysfunction in Lysosomal Storage Disorders: A Review

Mitochondrial dysfunction is emerging as an important contributory factor to the pathophysiology of lysosomal storage disorders (LSDs). The cause of mitochondrial dysfunction in LSDs appears to be multifactorial, although impaired mitophagy and oxidative stress appear to be common inhibitory mechani...

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Detalles Bibliográficos
Autores principales:	Stepien, Karolina M., Roncaroli, Federico, Turton, Nadia, Hendriksz, Christian J., Roberts, Mark, Heaton, Robert A., Hargreaves, Iain
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	MDPI 2020
Materias:	Review
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7463786/ https://www.ncbi.nlm.nih.gov/pubmed/32796538 http://dx.doi.org/10.3390/jcm9082596

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