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A dermatopathic Juvenile Dermatomyositis; An Unexpected Case in Childhood

Juvenile dermatomyositis (JDM) is a rare idiopathic inflammatory disease, which usually presents with skin rashes along with muscle weakness. We report a case of JDM in a 10- year-old girl with no skin manifestations presenting with progressive muscle weakness and fatigue. Further laboratory investi...

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Detalles Bibliográficos
Autores principales: HASSAS YEGANEH, Mehrnoush, AHMADI, Pooria, NILIPOUR, Yalda, MOUSAVI KHORSHIDI, Mohadese sadat, SINAEI, Reza, FATHI, Mohammad Reza, SHIARI, Reza
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Shahid Beheshti University of Medical Sciences 2020
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7468081/
https://www.ncbi.nlm.nih.gov/pubmed/32952586
Descripción
Sumario:Juvenile dermatomyositis (JDM) is a rare idiopathic inflammatory disease, which usually presents with skin rashes along with muscle weakness. We report a case of JDM in a 10- year-old girl with no skin manifestations presenting with progressive muscle weakness and fatigue. Further laboratory investigations, along with a muscle biopsy, confirmed the diagnosis of adermatopathic JDM. The patient was treated with intravenous immunoglobulin, corticosteroids, methotrexate, hydroxychloroquine, pamidronate, and rituximab. Following treatment, patients’ symptoms subsided, and she gained normal muscular strength over a year.