The Natural History of X-Linked Lymphoproliferative Disease (XLP1): Lessons from a Long-Term Survivor

X-linked lymphoproliferative disease (XLP1) is a rare primary immunodeficiency characterized by EBV-triggered immune dysregulation, lymphoproliferation, dysgammaglobulinemia, and lymphoma. Early childhood mortality from overwhelming inflammation is expected in most patients. The only curative therap...

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Detalles Bibliográficos
Autores principales: Jiang, Yike, Firan, Mihail, Nandiwada, Sarada L., Reyes, Anaid, Marsh, Rebecca A., Vogel, Tiphanie P., Hajjar, Joud
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Hindawi 2020
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7474360/
https://www.ncbi.nlm.nih.gov/pubmed/32908732
http://dx.doi.org/10.1155/2020/8841571

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