ADAMTS18 Deficiency Leads to Pulmonary Hypoplasia and Bronchial Microfibril Accumulation

ADAMTSs (a disintegrin and metalloproteinase with thrombospondin motifs) are secreted metalloproteinases that play a major role in the assembly and degradation of the extracellular matrix (ECM). In this study, we show that ADAMTS18, produced by the epithelial cells of distal airways and mesenchymal...

Descripción completa

Detalles Bibliográficos
Autores principales: Lu, Tiantian, Lin, Xiaotian, Pan, Yi-Hsuan, Yang, Ning, Ye, Shuai, Zhang, Qi, Wang, Caiyun, Zhu, Rui, Zhang, Tianhao, Wisniewski, Thomas M., Cao, Zhongwei, Ding, Bi-Sen, Dang, Suying, Zhang, Wei
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2020
Materias:
Article
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7476315/
https://www.ncbi.nlm.nih.gov/pubmed/32882513
http://dx.doi.org/10.1016/j.isci.2020.101472

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7476315/
https://www.ncbi.nlm.nih.gov/pubmed/32882513
http://dx.doi.org/10.1016/j.isci.2020.101472

Ejemplares similares