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Bilateral sudden sensorineural hearing loss with Sweet syndrome: A case report

INTRODUCTION: Sweet syndrome (SS) is an idiopathic autoimmune disease which has been associated with various extracutaneous manifestations. Otologic symptoms secondary to SS are characterized by bilateral, progressive, sensorineural hearing loss, which requires auditory rehabilitation with, for exam...

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Autores principales: You, Yeon Seok, Park, Sang Woo, Yun, Seok Kweon, Lee, Eun Jung
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Lippincott Williams & Wilkins 2020
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7478687/
https://www.ncbi.nlm.nih.gov/pubmed/32899098
http://dx.doi.org/10.1097/MD.0000000000022127
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author You, Yeon Seok
Park, Sang Woo
Yun, Seok Kweon
Lee, Eun Jung
author_facet You, Yeon Seok
Park, Sang Woo
Yun, Seok Kweon
Lee, Eun Jung
author_sort You, Yeon Seok
collection PubMed
description INTRODUCTION: Sweet syndrome (SS) is an idiopathic autoimmune disease which has been associated with various extracutaneous manifestations. Otologic symptoms secondary to SS are characterized by bilateral, progressive, sensorineural hearing loss, which requires auditory rehabilitation with, for example, cochlear implantation. PATIENT CONCERNS: A 43-year-old woman complaining of bilateral sudden hearing loss visited the Emergency Department of our University. Abrupt onset of fever peaking up to 40°C and vomiting accompanied the hearing loss and other associated symptoms were: tinnitus that sounded like a machine humming, mild dizziness, a painful rash (on the right upper eyelid, chest, back, forearms, and lower extremities), arthralgia in both the hip and knee joints, and vision loss in the right eye. The patient had no history of autoimmune diseases or surgery. DIAGNOSIS: Pure tone audiometry and biopsy on the skin lesion were performed. SS with bilateral sudden sensorineural hearing loss was confirmed. INTERVENTIONS: The patient was treated with intravenous prednisolone and topical steroids. OUTCOMES: After a week of treatment, skin lesions had improved. And 3 months after treatment, the hearing test showed full recovery. CONCLUSION: This case emphasizes the point that early diagnosis and timely treatment are essential for hearing recovery in patients with SS who have otologic symptoms.
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spelling pubmed-74786872020-09-24 Bilateral sudden sensorineural hearing loss with Sweet syndrome: A case report You, Yeon Seok Park, Sang Woo Yun, Seok Kweon Lee, Eun Jung Medicine (Baltimore) 6000 INTRODUCTION: Sweet syndrome (SS) is an idiopathic autoimmune disease which has been associated with various extracutaneous manifestations. Otologic symptoms secondary to SS are characterized by bilateral, progressive, sensorineural hearing loss, which requires auditory rehabilitation with, for example, cochlear implantation. PATIENT CONCERNS: A 43-year-old woman complaining of bilateral sudden hearing loss visited the Emergency Department of our University. Abrupt onset of fever peaking up to 40°C and vomiting accompanied the hearing loss and other associated symptoms were: tinnitus that sounded like a machine humming, mild dizziness, a painful rash (on the right upper eyelid, chest, back, forearms, and lower extremities), arthralgia in both the hip and knee joints, and vision loss in the right eye. The patient had no history of autoimmune diseases or surgery. DIAGNOSIS: Pure tone audiometry and biopsy on the skin lesion were performed. SS with bilateral sudden sensorineural hearing loss was confirmed. INTERVENTIONS: The patient was treated with intravenous prednisolone and topical steroids. OUTCOMES: After a week of treatment, skin lesions had improved. And 3 months after treatment, the hearing test showed full recovery. CONCLUSION: This case emphasizes the point that early diagnosis and timely treatment are essential for hearing recovery in patients with SS who have otologic symptoms. Lippincott Williams & Wilkins 2020-09-04 /pmc/articles/PMC7478687/ /pubmed/32899098 http://dx.doi.org/10.1097/MD.0000000000022127 Text en Copyright © 2020 the Author(s). Published by Wolters Kluwer Health, Inc. http://creativecommons.org/licenses/by/4.0 This is an open access article distributed under the Creative Commons Attribution License 4.0 (CCBY), which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited. http://creativecommons.org/licenses/by/4.0
spellingShingle 6000
You, Yeon Seok
Park, Sang Woo
Yun, Seok Kweon
Lee, Eun Jung
Bilateral sudden sensorineural hearing loss with Sweet syndrome: A case report
title Bilateral sudden sensorineural hearing loss with Sweet syndrome: A case report
title_full Bilateral sudden sensorineural hearing loss with Sweet syndrome: A case report
title_fullStr Bilateral sudden sensorineural hearing loss with Sweet syndrome: A case report
title_full_unstemmed Bilateral sudden sensorineural hearing loss with Sweet syndrome: A case report
title_short Bilateral sudden sensorineural hearing loss with Sweet syndrome: A case report
title_sort bilateral sudden sensorineural hearing loss with sweet syndrome: a case report
topic 6000
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7478687/
https://www.ncbi.nlm.nih.gov/pubmed/32899098
http://dx.doi.org/10.1097/MD.0000000000022127
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