Pigmented villonodular synovitis associated with developmental dysplasia of the hip: A case report

INTRODUCTION: Pigmented villonodular synovitis (PVNS) of the hip joint associated with developmental dysplasia of the hip joint (DDH) is an extremely rare co-presentation. The aim of this study is to report a case of PVNS associated with DDH. PRESENTATION OF CASE: A 26-year-old women, a known case of DDH, presented with progressive right hip pain for one month duration. She was able to perform all the right hip movements with limitation due to pain. Plain radiographs showed a hip dislocation. Through a posterior incision, a mass of brown fibro-fatty soft tissue emerged. The specimen was sent for histopathological examination, The findings were variable mixture of giant cells, hemosiderin, and brown pigmentation in the synoviocyte cytoplasm. DISCUSSION: Although both conditions were previously described separately, the significance of co-incidence of DDH and PVNS is not well understood due to the rarity of the association. CONCLUSION: Co-incidence of DDH with PVNS is an extremely rare finding but could be safely managed if caught early in the beginning of the disease.