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Dystrophin Is Required for the Proper Timing in Retinal Histogenesis: A Thorough Investigation on the mdx Mouse Model of Duchenne Muscular Dystrophy
Duchenne muscular dystrophy (DMD) is a lethal X-linked muscular disease caused by defective expression of the cytoskeletal protein dystrophin (Dp427). Selected autonomic and central neurons, including retinal neurons, express Dp427 and/or dystrophin shorter isoforms. Because of this, DMD patients ma...
Autores principales: | Persiconi, Irene, Cosmi, Francesca, Guadagno, Noemi Antonella, Lupo, Giuseppe, De Stefano, Maria Egle |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Frontiers Media S.A.
2020
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7487415/ https://www.ncbi.nlm.nih.gov/pubmed/32982660 http://dx.doi.org/10.3389/fnins.2020.00760 |
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