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Retained primary teeth in STAT3 hyper-IgE syndrome: early intervention in childhood is essential

BACKGROUND: STAT3 hyper-IgE syndrome (STAT3-HIES) is a rare primary immunodeficiency that clinically overlaps with atopic dermatitis. In addition to eczema, elevated serum-IgE, and recurrent infections, STAT3-HIES patients suffer from characteristic facies, midline defects, and retained primary teet...

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Detalles Bibliográficos
Autores principales:	Meixner, Iris, Hagl, Beate, Kröner, Carolin I., Spielberger, Benedikt D., Paschos, Ekaterini, Dückers, Gregor, Niehues, Tim, Hesse, Ronny, Renner, Ellen D.
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	BioMed Central 2020
Materias:	Research
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7488068/ https://www.ncbi.nlm.nih.gov/pubmed/32912316 http://dx.doi.org/10.1186/s13023-020-01516-3

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