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CLASSIFICATION AND MANAGEMENT OF HEMIFACIAL MICROSOMIA: A LITERATURE REVIEW
Hemifacial microsomia (HFM) is the 2(nd) most common craniofacial birth defect after cleft lip and palate. It is said to arise from the 1(st) & 2(nd) intrauterine branchial arches. HFM is believed by many experts to be congenital but not inherited as most patients afflicted have no previous fami...
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Association of Resident Doctors (ARD), University College Hospital, Ibadan
2020
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7513375/ https://www.ncbi.nlm.nih.gov/pubmed/33071690 |
Sumario: | Hemifacial microsomia (HFM) is the 2(nd) most common craniofacial birth defect after cleft lip and palate. It is said to arise from the 1(st) & 2(nd) intrauterine branchial arches. HFM is believed by many experts to be congenital but not inherited as most patients afflicted have no previous family history. It also known as craniofacial microstomia with cranial involvement. The real cause is unknown but largely blamed on hemorrhage of the stapaedial artery. The phenotypic expression is variable from mild to severe involving many structures such as bone, nerve, muscular tissues and soft tissue. Facial structures commonly affected include the ears, the mouth and the mandible. Mostly unilateral but bilateral have been reported. However, not much is known about this condition in sub-Saharan Africa. Multidisciplinary team management is the general consensus for optimal care. Awareness in sub-Saharan Africa of this disorder is still evolving. This review identifies various classifications, diagnoses, investigations, treatment and timelines for management of HFM. The aim of the current review was to discuss the diverse controversies, classification, diagnosis and treatment of HFM so as to increase the understanding of this condition. |
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