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Lyso-glycosphingolipids: presence and consequences

Lyso-glycosphingolipids are generated in excess in glycosphingolipid storage disorders. In the course of these pathologies glycosylated sphingolipid species accumulate within lysosomes due to flaws in the respective lipid degrading machinery. Deacylation of accumulating glycosphingolipids drives the...

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Detalles Bibliográficos
Autores principales:	van Eijk, Marco, Ferraz, Maria J., Boot, Rolf G., Aerts, Johannes M.F.G.
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Portland Press Ltd. 2020
Materias:	Molecular Bases of Health & Disease
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7517347/ https://www.ncbi.nlm.nih.gov/pubmed/32808655 http://dx.doi.org/10.1042/EBC20190090

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