Challenges and experiences in correcting scoliosis of a patient with Marfan Syndrome: A case report

INTRODUCTION: Although common, it is not always easy to treat scoliosis in Marfan Syndrome. The distinguished anatomical components make it harder to treat the entity, albeit managing the whole patient. It is already widely known that the correction requires an immersive preoperative planning as well as a vast surgeon experience in order to preparedly face the possible that may happen intra operatively and post operatively. CASE PRESENTATION: We present a case of patient with Marfan’s syndrome presenting to our outpatient clinic with scoliosis deformity since 4 years ago. Patient also had cardiovascular problems. At the time of visitation, patient had a main thoracic Cobb Angle of 87.5° and lumbar Cobb Angle of 76.7°. RESULT: We did a one-step surgical correction of scoliosis. We managed to acutely correct the scoliosis and maintain the correction by using a posterior stabilization. Afterwards patient was well conditioned and was discharged around 6 days later. The follow up was good, patient had no neurological deficits, and was able to walk without walker after 1 month. DISCUSSION: Marfan Syndrome with scoliosis requires a good preoperative planning so that we may avoid unnecessary complications. It is still possible to do an acute correction for scoliosis that is severe and still maintain little to no complications rate.