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Subclinical effects of long‐chain fatty acid β‐oxidation deficiency on the adult heart: A case‐control magnetic resonance study
Cardiomyopathy can be a severe complication in patients with long‐chain fatty acid β‐oxidation disorders (LCFAOD), particularly during episodes of metabolic derangement. It is unknown whether latent cardiac abnormalities exist in adult patients. To investigate cardiac involvement in LCFAOD, we used...
Autores principales: | Knottnerus, Suzan J. G., Bleeker, Jeannette C., Ferdinandusse, Sacha, Houtkooper, Riekelt H., Langeveld, Mirjam, Nederveen, Aart J., Strijkers, Gustav J., Visser, Gepke, Wanders, Ronald J. A., Wijburg, Frits A., Boekholdt, S. Matthijs, Bakermans, Adrianus J. |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
John Wiley & Sons, Inc.
2020
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7539973/ https://www.ncbi.nlm.nih.gov/pubmed/32463482 http://dx.doi.org/10.1002/jimd.12266 |
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