Cargando…
Pathological evaluation of rats carrying in-frame mutations in the dystrophin gene: a new model of Becker muscular dystrophy
Dystrophin, encoded by the DMD gene on the X chromosome, stabilizes the sarcolemma by linking the actin cytoskeleton with the dystrophin-glycoprotein complex (DGC). In-frame mutations in DMD cause a milder form of X-linked muscular dystrophy, called Becker muscular dystrophy (BMD), characterized by...
Autores principales: | Teramoto, Naomi, Sugihara, Hidetoshi, Yamanouchi, Keitaro, Nakamura, Katsuyuki, Kimura, Koichi, Okano, Tomoko, Shiga, Takanori, Shirakawa, Taku, Matsuo, Masafumi, Nagata, Tetsuya, Daimon, Masao, Matsuwaki, Takashi, Nishihara, Masugi |
---|---|
Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
The Company of Biologists Ltd
2020
|
Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7541341/ https://www.ncbi.nlm.nih.gov/pubmed/32859695 http://dx.doi.org/10.1242/dmm.044701 |
Ejemplares similares
-
Cellular senescence-mediated exacerbation of Duchenne muscular dystrophy
por: Sugihara, Hidetoshi, et al.
Publicado: (2020) -
Oxidative stress-mediated senescence in mesenchymal progenitor cells causes the loss of their fibro/adipogenic potential and abrogates myoblast fusion
por: Sugihara, Hidetoshi, et al.
Publicado: (2018) -
Loss of p16/Ink4a drives high frequency of rhabdomyosarcoma in a rat model of Duchenne muscular dystrophy
por: TERAMOTO, Naomi, et al.
Publicado: (2021) -
Progranulin deficiency leads to prolonged persistence of macrophages,
accompanied with myofiber hypertrophy in regenerating muscle
por: SUGIHARA, Hidetoshi, et al.
Publicado: (2017) -
Differentiation of skeletal muscle Mesenchymal progenitor cells to myofibroblasts is reversible
por: Takeuchi, Shiho, et al.
Publicado: (2020)