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Image report: Extensive disseminated thoracolumbosacral myxopapillary ependymoma

BACKGROUND: Myxopapillary ependymoma occurs more frequently in adults, but is found in the first two decades of life in around 8–20% of patients. Tumors are usually benign with low likelihood for dissemination. CASE DESCRIPTION: We describe a case of a 13-year-old boy who presented with progressive...

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Detalles Bibliográficos
Autores principales: Vongsfak, Jirapong, Jetjumnong, Chumpon, Cullen, James
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Scientific Scholar 2020
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7568109/
https://www.ncbi.nlm.nih.gov/pubmed/33093974
http://dx.doi.org/10.25259/SNI_390_2020
Descripción
Sumario:BACKGROUND: Myxopapillary ependymoma occurs more frequently in adults, but is found in the first two decades of life in around 8–20% of patients. Tumors are usually benign with low likelihood for dissemination. CASE DESCRIPTION: We describe a case of a 13-year-old boy who presented with progressive kyphosis and bilateral weakness of the lower limbs. MRI shows a thoracolumbosacral intradural tumor with invasion of sacral neural foramina and dissemination to the cervicothoracic region. The patient received T10-L5 laminectomy with subtotal tumor resection. Pathological examination revealed myxopapillary ependymoma. After surgical resection, the patient underwent physical therapy with whole spinal radiotherapy for disease control. CONCLUSION: Spinal myxopapillary ependymomas are usually benign and slow-growing tumors. This case illustrates an extensive and disseminated myxopapillary ependymoma.