Orbital hybrid peripheral nerve sheath tumors

Hybrid peripheral nerve sheath tumors (HPNST) are recently classified tumors from the World Health Organization Classification of soft tissue tumors that display combined features of more than one peripheral nerve sheath tumor. Acknowledgment is important because of its association with the developm...

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Detalles Bibliográficos
Autores principales: Leung, Kai Ching Peter, Ko, Tak Chuen Simon
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Wolters Kluwer - Medknow 2020
Materias:
Review Article
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7585476/
https://www.ncbi.nlm.nih.gov/pubmed/33110748
http://dx.doi.org/10.4103/tjo.tjo_28_20
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author Leung, Kai Ching Peter
Ko, Tak Chuen Simon
author_facet Leung, Kai Ching Peter
Ko, Tak Chuen Simon
author_sort Leung, Kai Ching Peter
collection PubMed
description Hybrid peripheral nerve sheath tumors (HPNST) are recently classified tumors from the World Health Organization Classification of soft tissue tumors that display combined features of more than one peripheral nerve sheath tumor. Acknowledgment is important because of its association with the development of neurofibromatosis type 1, type 2, and schwannomatosis. Orbital involvement is rare and only six cases of HPNST have been documented on literature. This article serves to review the pathophysiology, clinical manifestation, diagnosis, treatment, and prognosis of this infrequent but important orbital tumor.
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spelling pubmed-75854762020-10-26 Orbital hybrid peripheral nerve sheath tumors Leung, Kai Ching Peter Ko, Tak Chuen Simon Taiwan J Ophthalmol Review Article Hybrid peripheral nerve sheath tumors (HPNST) are recently classified tumors from the World Health Organization Classification of soft tissue tumors that display combined features of more than one peripheral nerve sheath tumor. Acknowledgment is important because of its association with the development of neurofibromatosis type 1, type 2, and schwannomatosis. Orbital involvement is rare and only six cases of HPNST have been documented on literature. This article serves to review the pathophysiology, clinical manifestation, diagnosis, treatment, and prognosis of this infrequent but important orbital tumor. Wolters Kluwer - Medknow 2020-07-27 /pmc/articles/PMC7585476/ /pubmed/33110748 http://dx.doi.org/10.4103/tjo.tjo_28_20 Text en Copyright: © 2020 Taiwan J Ophthalmol http://creativecommons.org/licenses/by-nc-sa/4.0 This is an open access journal, and articles are distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 4.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as appropriate credit is given and the new creations are licensed under the identical terms.
spellingShingle Review Article
Leung, Kai Ching Peter
Ko, Tak Chuen Simon
Orbital hybrid peripheral nerve sheath tumors
title Orbital hybrid peripheral nerve sheath tumors
title_full Orbital hybrid peripheral nerve sheath tumors
title_fullStr Orbital hybrid peripheral nerve sheath tumors
title_full_unstemmed Orbital hybrid peripheral nerve sheath tumors
title_short Orbital hybrid peripheral nerve sheath tumors
title_sort orbital hybrid peripheral nerve sheath tumors
topic Review Article
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7585476/
https://www.ncbi.nlm.nih.gov/pubmed/33110748
http://dx.doi.org/10.4103/tjo.tjo_28_20
work_keys_str_mv AT leungkaichingpeter orbitalhybridperipheralnervesheathtumors
AT kotakchuensimon orbitalhybridperipheralnervesheathtumors

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