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How Altered Ribosome Production Can Cause or Contribute to Human Disease: The Spectrum of Ribosomopathies

A number of different defects in the process of ribosome production can lead to a diversified spectrum of disorders that are collectively identified as ribosomopathies. The specific factors involved may either play a role only in ribosome biogenesis or have additional extra-ribosomal functions, maki...

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Detalles Bibliográficos
Autores principales: Venturi, Giulia, Montanaro, Lorenzo
Formato: Online Artículo Texto
Lenguaje:English
Publicado: MDPI 2020
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7602531/
https://www.ncbi.nlm.nih.gov/pubmed/33076379
http://dx.doi.org/10.3390/cells9102300
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author Venturi, Giulia
Montanaro, Lorenzo
author_facet Venturi, Giulia
Montanaro, Lorenzo
author_sort Venturi, Giulia
collection PubMed
description A number of different defects in the process of ribosome production can lead to a diversified spectrum of disorders that are collectively identified as ribosomopathies. The specific factors involved may either play a role only in ribosome biogenesis or have additional extra-ribosomal functions, making it difficult to ascribe the pathogenesis of the disease specifically to an altered ribosome biogenesis, even if the latter is clearly affected. We reviewed the available literature in the field from this point of view with the aim of distinguishing, among ribosomopathies, the ones due to specific alterations in the process of ribosome production from those characterized by a multifactorial pathogenesis.
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spelling pubmed-76025312020-11-01 How Altered Ribosome Production Can Cause or Contribute to Human Disease: The Spectrum of Ribosomopathies Venturi, Giulia Montanaro, Lorenzo Cells Review A number of different defects in the process of ribosome production can lead to a diversified spectrum of disorders that are collectively identified as ribosomopathies. The specific factors involved may either play a role only in ribosome biogenesis or have additional extra-ribosomal functions, making it difficult to ascribe the pathogenesis of the disease specifically to an altered ribosome biogenesis, even if the latter is clearly affected. We reviewed the available literature in the field from this point of view with the aim of distinguishing, among ribosomopathies, the ones due to specific alterations in the process of ribosome production from those characterized by a multifactorial pathogenesis. MDPI 2020-10-15 /pmc/articles/PMC7602531/ /pubmed/33076379 http://dx.doi.org/10.3390/cells9102300 Text en © 2020 by the authors. Licensee MDPI, Basel, Switzerland. This article is an open access article distributed under the terms and conditions of the Creative Commons Attribution (CC BY) license (http://creativecommons.org/licenses/by/4.0/).
spellingShingle Review
Venturi, Giulia
Montanaro, Lorenzo
How Altered Ribosome Production Can Cause or Contribute to Human Disease: The Spectrum of Ribosomopathies
title How Altered Ribosome Production Can Cause or Contribute to Human Disease: The Spectrum of Ribosomopathies
title_full How Altered Ribosome Production Can Cause or Contribute to Human Disease: The Spectrum of Ribosomopathies
title_fullStr How Altered Ribosome Production Can Cause or Contribute to Human Disease: The Spectrum of Ribosomopathies
title_full_unstemmed How Altered Ribosome Production Can Cause or Contribute to Human Disease: The Spectrum of Ribosomopathies
title_short How Altered Ribosome Production Can Cause or Contribute to Human Disease: The Spectrum of Ribosomopathies
title_sort how altered ribosome production can cause or contribute to human disease: the spectrum of ribosomopathies
topic Review
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7602531/
https://www.ncbi.nlm.nih.gov/pubmed/33076379
http://dx.doi.org/10.3390/cells9102300
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