Optic nerve Hemangioblastoma with bilateral frontal lobe Oedema: a case report

BACKGROUND: Hemangioblastomas are rare benign tumours that are most commonly detected in the subtentorium or spinal cord. Optic nerve hemangioblastoma is very rare and is most commonly associated with Von Hippel-Lindau (VHL) syndrome. CASE PRESENTATION: Here, we report a case of hemangioblastoma of...

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Autores principales: Xu, Shujia, Li, Qian, Bian, Bingyang, Zhou, Hongli, Li, Dan
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BioMed Central 2020
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7640410/
https://www.ncbi.nlm.nih.gov/pubmed/33143685
http://dx.doi.org/10.1186/s12886-020-01706-4
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author Xu, Shujia
Li, Qian
Bian, Bingyang
Zhou, Hongli
Li, Dan
author_facet Xu, Shujia
Li, Qian
Bian, Bingyang
Zhou, Hongli
Li, Dan
author_sort Xu, Shujia
collection PubMed
description BACKGROUND: Hemangioblastomas are rare benign tumours that are most commonly detected in the subtentorium or spinal cord. Optic nerve hemangioblastoma is very rare and is most commonly associated with Von Hippel-Lindau (VHL) syndrome. CASE PRESENTATION: Here, we report a case of hemangioblastoma of the optic nerve with bilateral frontal lobe oedema without VHL syndrome, which has not yet been reported. A 51-year-old woman presented with progressive and painless deteriorating vision in the left eye. Magnetic resonance imaging showed a mass at the back of the left orbital optic nerve. Endoscopic-assisted intraorbital tumour resection was performed successfully. The pathological diagnosis was left optic nerve hemangioblastoma. CONCLUSIONS: This is the first reported case of optic nerve hemangioblastoma (HBL) with bilateral frontal lobe oedema.
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spelling pubmed-76404102020-11-04 Optic nerve Hemangioblastoma with bilateral frontal lobe Oedema: a case report Xu, Shujia Li, Qian Bian, Bingyang Zhou, Hongli Li, Dan BMC Ophthalmol Case Report BACKGROUND: Hemangioblastomas are rare benign tumours that are most commonly detected in the subtentorium or spinal cord. Optic nerve hemangioblastoma is very rare and is most commonly associated with Von Hippel-Lindau (VHL) syndrome. CASE PRESENTATION: Here, we report a case of hemangioblastoma of the optic nerve with bilateral frontal lobe oedema without VHL syndrome, which has not yet been reported. A 51-year-old woman presented with progressive and painless deteriorating vision in the left eye. Magnetic resonance imaging showed a mass at the back of the left orbital optic nerve. Endoscopic-assisted intraorbital tumour resection was performed successfully. The pathological diagnosis was left optic nerve hemangioblastoma. CONCLUSIONS: This is the first reported case of optic nerve hemangioblastoma (HBL) with bilateral frontal lobe oedema. BioMed Central 2020-11-03 /pmc/articles/PMC7640410/ /pubmed/33143685 http://dx.doi.org/10.1186/s12886-020-01706-4 Text en © The Author(s) 2020 Open AccessThis article is licensed under a Creative Commons Attribution 4.0 International License, which permits use, sharing, adaptation, distribution and reproduction in any medium or format, as long as you give appropriate credit to the original author(s) and the source, provide a link to the Creative Commons licence, and indicate if changes were made. The images or other third party material in this article are included in the article's Creative Commons licence, unless indicated otherwise in a credit line to the material. If material is not included in the article's Creative Commons licence and your intended use is not permitted by statutory regulation or exceeds the permitted use, you will need to obtain permission directly from the copyright holder. To view a copy of this licence, visit http://creativecommons.org/licenses/by/4.0/. The Creative Commons Public Domain Dedication waiver (http://creativecommons.org/publicdomain/zero/1.0/) applies to the data made available in this article, unless otherwise stated in a credit line to the data.
spellingShingle Case Report
Xu, Shujia
Li, Qian
Bian, Bingyang
Zhou, Hongli
Li, Dan
Optic nerve Hemangioblastoma with bilateral frontal lobe Oedema: a case report
title Optic nerve Hemangioblastoma with bilateral frontal lobe Oedema: a case report
title_full Optic nerve Hemangioblastoma with bilateral frontal lobe Oedema: a case report
title_fullStr Optic nerve Hemangioblastoma with bilateral frontal lobe Oedema: a case report
title_full_unstemmed Optic nerve Hemangioblastoma with bilateral frontal lobe Oedema: a case report
title_short Optic nerve Hemangioblastoma with bilateral frontal lobe Oedema: a case report
title_sort optic nerve hemangioblastoma with bilateral frontal lobe oedema: a case report
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7640410/
https://www.ncbi.nlm.nih.gov/pubmed/33143685
http://dx.doi.org/10.1186/s12886-020-01706-4
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AT bianbingyang opticnervehemangioblastomawithbilateralfrontallobeoedemaacasereport
AT zhouhongli opticnervehemangioblastomawithbilateralfrontallobeoedemaacasereport
AT lidan opticnervehemangioblastomawithbilateralfrontallobeoedemaacasereport

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