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Autoimmune Hepatitis in a Patient With Common Variable Immunodeficiency

Common variable immunodeficiency (CVID), a condition characterized by impaired antibody production, is paradoxically associated with various autoimmune disorders. The most common causes of liver disease in patients with CVID are nodular regenerative hyperplasia, granulomatous infiltration of the liv...

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Detalles Bibliográficos
Autores principales: Pollock, Galia, Sharma, Aditya, GY, Minuk
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Wolters Kluwer 2020
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7665256/
https://www.ncbi.nlm.nih.gov/pubmed/33204738
http://dx.doi.org/10.14309/crj.0000000000000467
Descripción
Sumario:Common variable immunodeficiency (CVID), a condition characterized by impaired antibody production, is paradoxically associated with various autoimmune disorders. The most common causes of liver disease in patients with CVID are nodular regenerative hyperplasia, granulomatous infiltration of the liver, and chronic viral hepatitis. We present a case of autoimmune hepatitis in a patient with CVID.