A Rare Cause of Pulmonary Hypertension in a 4-Year-Old Toddler: Association of Cor Triatriatum Sinister and Pulmonary Arteriovenous Malformation

Cor triatriatum sinister is a rare congenital cardiac anomaly. The anomaly is caused by a fibromuscular membrane that divides the left atrium into two cavities. This membrane can lead to the obstruction of left atrial flow and also create pulmonary venous hypertension. Pulmonary arteriovenous malfor...

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Autores principales: Yozgat, Can Yilmaz, Cakir, Erkan, Yazan, Hakan, Temur, Hafize Otcu, Yakut, Kahraman, Yozgat, Yilmaz
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Hindawi 2020
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7673912/
https://www.ncbi.nlm.nih.gov/pubmed/33224546
http://dx.doi.org/10.1155/2020/8825215
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author Yozgat, Can Yilmaz
Cakir, Erkan
Yazan, Hakan
Temur, Hafize Otcu
Yakut, Kahraman
Yozgat, Yilmaz
author_facet Yozgat, Can Yilmaz
Cakir, Erkan
Yazan, Hakan
Temur, Hafize Otcu
Yakut, Kahraman
Yozgat, Yilmaz
author_sort Yozgat, Can Yilmaz
collection PubMed
description Cor triatriatum sinister is a rare congenital cardiac anomaly. The anomaly is caused by a fibromuscular membrane that divides the left atrium into two cavities. This membrane can lead to the obstruction of left atrial flow and also create pulmonary venous hypertension. Pulmonary arteriovenous malformation (PAVM) is notorious for its aberrant blood flow between the pulmonary arteries and veins. Herein, we report a case of a 4-year-old toddler who had a unique form of pulmonary hypertension presenting with cor triatriatum sinister and diffuse PAVM. After the surgical treatment of cor triatriatum sinister, both pulmonary arteriovenous malformation and pulmonary hypertension disappeared.
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spelling pubmed-76739122020-11-19 A Rare Cause of Pulmonary Hypertension in a 4-Year-Old Toddler: Association of Cor Triatriatum Sinister and Pulmonary Arteriovenous Malformation Yozgat, Can Yilmaz Cakir, Erkan Yazan, Hakan Temur, Hafize Otcu Yakut, Kahraman Yozgat, Yilmaz Case Rep Pediatr Case Report Cor triatriatum sinister is a rare congenital cardiac anomaly. The anomaly is caused by a fibromuscular membrane that divides the left atrium into two cavities. This membrane can lead to the obstruction of left atrial flow and also create pulmonary venous hypertension. Pulmonary arteriovenous malformation (PAVM) is notorious for its aberrant blood flow between the pulmonary arteries and veins. Herein, we report a case of a 4-year-old toddler who had a unique form of pulmonary hypertension presenting with cor triatriatum sinister and diffuse PAVM. After the surgical treatment of cor triatriatum sinister, both pulmonary arteriovenous malformation and pulmonary hypertension disappeared. Hindawi 2020-11-11 /pmc/articles/PMC7673912/ /pubmed/33224546 http://dx.doi.org/10.1155/2020/8825215 Text en Copyright © 2020 Can Yilmaz Yozgat et al. https://creativecommons.org/licenses/by/4.0/ This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Yozgat, Can Yilmaz
Cakir, Erkan
Yazan, Hakan
Temur, Hafize Otcu
Yakut, Kahraman
Yozgat, Yilmaz
A Rare Cause of Pulmonary Hypertension in a 4-Year-Old Toddler: Association of Cor Triatriatum Sinister and Pulmonary Arteriovenous Malformation
title A Rare Cause of Pulmonary Hypertension in a 4-Year-Old Toddler: Association of Cor Triatriatum Sinister and Pulmonary Arteriovenous Malformation
title_full A Rare Cause of Pulmonary Hypertension in a 4-Year-Old Toddler: Association of Cor Triatriatum Sinister and Pulmonary Arteriovenous Malformation
title_fullStr A Rare Cause of Pulmonary Hypertension in a 4-Year-Old Toddler: Association of Cor Triatriatum Sinister and Pulmonary Arteriovenous Malformation
title_full_unstemmed A Rare Cause of Pulmonary Hypertension in a 4-Year-Old Toddler: Association of Cor Triatriatum Sinister and Pulmonary Arteriovenous Malformation
title_short A Rare Cause of Pulmonary Hypertension in a 4-Year-Old Toddler: Association of Cor Triatriatum Sinister and Pulmonary Arteriovenous Malformation
title_sort rare cause of pulmonary hypertension in a 4-year-old toddler: association of cor triatriatum sinister and pulmonary arteriovenous malformation
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7673912/
https://www.ncbi.nlm.nih.gov/pubmed/33224546
http://dx.doi.org/10.1155/2020/8825215
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