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Quantitative proteomics reveal lineage-specific protein profiles in iPSC-derived Marfan syndrome smooth muscle cells
Marfan syndrome (MFS) is a connective tissue disorder caused by mutations in the FBN1 gene that produces wide disease phenotypic variability. The lack of ample genotype–phenotype correlation hinders translational study development aimed at improving disease prognosis. In response to this need, an in...
Autores principales: | Iosef, Cristiana, Pedroza, Albert J., Cui, Jason Z., Dalal, Alex R., Arakawa, Mamoru, Tashima, Yasushi, Koyano, Tiffany K., Burdon, Grayson, Churovich, Samantha M. P., Orrick, Joshua O., Pariani, Mitchel, Fischbein, Michael P. |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Nature Publishing Group UK
2020
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7683538/ https://www.ncbi.nlm.nih.gov/pubmed/33230159 http://dx.doi.org/10.1038/s41598-020-77274-w |
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