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Hyper IgE syndrome (Job syndrome) in Syria: a case report
Hyper IgE syndrome (HIES) is a medical condition that can be sporadic or hereditary. It consists of multiple overlapping primary immunodeficiency conditions and is characterized by a classical triad of high immunoglobulin E (IgE) levels, recurrent pneumonia with pneumatocele and recurrent cold skin...
Autores principales: | , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Oxford University Press
2020
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7685025/ https://www.ncbi.nlm.nih.gov/pubmed/33269088 http://dx.doi.org/10.1093/omcr/omaa106 |
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author | Awad, Rama Kakaje, Ameer |
author_facet | Awad, Rama Kakaje, Ameer |
author_sort | Awad, Rama |
collection | PubMed |
description | Hyper IgE syndrome (HIES) is a medical condition that can be sporadic or hereditary. It consists of multiple overlapping primary immunodeficiency conditions and is characterized by a classical triad of high immunoglobulin E (IgE) levels, recurrent pneumonia with pneumatocele and recurrent cold skin abscesses from staphylococcus infections. Eosinophilia is also common in HIES patients. HIES is often underdiagnosed in Syria as it cannot be confirmed without genetic testing, which is unavailable across Syria for HIES. We present the first case from Syria of a suspected child with HIES that has some additional distinct features. Other cases in a regional country carried atypical novel mutations, which may indicate that these mutations may exist in Syria as well. However, our case had findings that were not reported with other HIES cases. Determining these genes in the case presented was not possible, and future studies need to overcome this hurdle. |
format | Online Article Text |
id | pubmed-7685025 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2020 |
publisher | Oxford University Press |
record_format | MEDLINE/PubMed |
spelling | pubmed-76850252020-12-01 Hyper IgE syndrome (Job syndrome) in Syria: a case report Awad, Rama Kakaje, Ameer Oxf Med Case Reports Case Report Hyper IgE syndrome (HIES) is a medical condition that can be sporadic or hereditary. It consists of multiple overlapping primary immunodeficiency conditions and is characterized by a classical triad of high immunoglobulin E (IgE) levels, recurrent pneumonia with pneumatocele and recurrent cold skin abscesses from staphylococcus infections. Eosinophilia is also common in HIES patients. HIES is often underdiagnosed in Syria as it cannot be confirmed without genetic testing, which is unavailable across Syria for HIES. We present the first case from Syria of a suspected child with HIES that has some additional distinct features. Other cases in a regional country carried atypical novel mutations, which may indicate that these mutations may exist in Syria as well. However, our case had findings that were not reported with other HIES cases. Determining these genes in the case presented was not possible, and future studies need to overcome this hurdle. Oxford University Press 2020-11-24 /pmc/articles/PMC7685025/ /pubmed/33269088 http://dx.doi.org/10.1093/omcr/omaa106 Text en © The Author(s) 2020. Published by Oxford University Press. All rights reserved. For Permissions, please email: journals.permissions@oup.com http://creativecommons.org/licenses/by-nc/4.0/ This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/4.0/), which permits non-commercial re-use, distribution, and reproduction in any medium, provided the original work is properly cited. For commercial re-use, please contact journals.permissions@oup.com |
spellingShingle | Case Report Awad, Rama Kakaje, Ameer Hyper IgE syndrome (Job syndrome) in Syria: a case report |
title | Hyper IgE syndrome (Job syndrome) in Syria: a case report |
title_full | Hyper IgE syndrome (Job syndrome) in Syria: a case report |
title_fullStr | Hyper IgE syndrome (Job syndrome) in Syria: a case report |
title_full_unstemmed | Hyper IgE syndrome (Job syndrome) in Syria: a case report |
title_short | Hyper IgE syndrome (Job syndrome) in Syria: a case report |
title_sort | hyper ige syndrome (job syndrome) in syria: a case report |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7685025/ https://www.ncbi.nlm.nih.gov/pubmed/33269088 http://dx.doi.org/10.1093/omcr/omaa106 |
work_keys_str_mv | AT awadrama hyperigesyndromejobsyndromeinsyriaacasereport AT kakajeameer hyperigesyndromejobsyndromeinsyriaacasereport |