Anesthetic Management of Living-Donor Renal Transplantation in a Patient With Epstein Syndrome Using Rotational Thromboelastometry: A Case Report

Epstein syndrome is a myosin heavy chain 9 (MYH9)-related disorder characterized by hearing loss and macrothrombocytopenia with renal failure, which usually requires platelet transfusion during surgery. We report the case of a 22-year-old man who underwent living-donor renal transplantation without...

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Autores principales: Higashi, Midoriko, Kaku, Keizo, Okabe, Yasuhiro, Yamaura, Ken
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Lippincott Williams & Wilkins 2020
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7688077/
https://www.ncbi.nlm.nih.gov/pubmed/33236872
http://dx.doi.org/10.1213/XAA.0000000000001350
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author Higashi, Midoriko
Kaku, Keizo
Okabe, Yasuhiro
Yamaura, Ken
author_facet Higashi, Midoriko
Kaku, Keizo
Okabe, Yasuhiro
Yamaura, Ken
author_sort Higashi, Midoriko
collection PubMed
description Epstein syndrome is a myosin heavy chain 9 (MYH9)-related disorder characterized by hearing loss and macrothrombocytopenia with renal failure, which usually requires platelet transfusion during surgery. We report the case of a 22-year-old man who underwent living-donor renal transplantation without platelet transfusion using rotational thromboelastometry (ROTEM) monitoring. His intraoperative laboratory coagulation findings were a platelet count of 28–31 × 10(9)/L based on microscopy and fibrinogen of 256 mg/dL. However, his extrinsic pathway evaluations by ROTEM were normal. The estimated blood loss during the operation was 150 mL, and the patient showed no bleeding complications without platelet transfusion.
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spelling pubmed-76880772020-12-01 Anesthetic Management of Living-Donor Renal Transplantation in a Patient With Epstein Syndrome Using Rotational Thromboelastometry: A Case Report Higashi, Midoriko Kaku, Keizo Okabe, Yasuhiro Yamaura, Ken A A Pract Case Report Epstein syndrome is a myosin heavy chain 9 (MYH9)-related disorder characterized by hearing loss and macrothrombocytopenia with renal failure, which usually requires platelet transfusion during surgery. We report the case of a 22-year-old man who underwent living-donor renal transplantation without platelet transfusion using rotational thromboelastometry (ROTEM) monitoring. His intraoperative laboratory coagulation findings were a platelet count of 28–31 × 10(9)/L based on microscopy and fibrinogen of 256 mg/dL. However, his extrinsic pathway evaluations by ROTEM were normal. The estimated blood loss during the operation was 150 mL, and the patient showed no bleeding complications without platelet transfusion. Lippincott Williams & Wilkins 2020-11-19 /pmc/articles/PMC7688077/ /pubmed/33236872 http://dx.doi.org/10.1213/XAA.0000000000001350 Text en Copyright © 2020 The Author(s). Published by Wolters Kluwer Health, Inc. on behalf of the International Anesthesia Research Society. This is an open-access article distributed under the terms of the Creative Commons Attribution-Non Commercial-No Derivatives License 4.0 (CCBY-NC-ND) (http://creativecommons.org/licenses/by-nc-nd/4.0/) , where it is permissible to download and share the work provided it is properly cited. The work cannot be changed in any way or used commercially without permission from the journal.
spellingShingle Case Report
Higashi, Midoriko
Kaku, Keizo
Okabe, Yasuhiro
Yamaura, Ken
Anesthetic Management of Living-Donor Renal Transplantation in a Patient With Epstein Syndrome Using Rotational Thromboelastometry: A Case Report
title Anesthetic Management of Living-Donor Renal Transplantation in a Patient With Epstein Syndrome Using Rotational Thromboelastometry: A Case Report
title_full Anesthetic Management of Living-Donor Renal Transplantation in a Patient With Epstein Syndrome Using Rotational Thromboelastometry: A Case Report
title_fullStr Anesthetic Management of Living-Donor Renal Transplantation in a Patient With Epstein Syndrome Using Rotational Thromboelastometry: A Case Report
title_full_unstemmed Anesthetic Management of Living-Donor Renal Transplantation in a Patient With Epstein Syndrome Using Rotational Thromboelastometry: A Case Report
title_short Anesthetic Management of Living-Donor Renal Transplantation in a Patient With Epstein Syndrome Using Rotational Thromboelastometry: A Case Report
title_sort anesthetic management of living-donor renal transplantation in a patient with epstein syndrome using rotational thromboelastometry: a case report
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7688077/
https://www.ncbi.nlm.nih.gov/pubmed/33236872
http://dx.doi.org/10.1213/XAA.0000000000001350
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