Pulmonary Artery Intimal Sarcoma: A Deadly Diagnosis in Disguise

Pulmonary artery intimal sarcoma (PAIS) is a very rare tumour. The prevalence of PAIS is estimated to be between 0.001% and 0.003%, but this may be an underestimation because of potential misdiagnosis due to its similar presentation to that of pulmonary thromboembolism. The prognosis is very poor, w...

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Detalles Bibliográficos
Autores principales: Rabbani, Mohamad, Hafiz, Ahmed, Algadheeb, Muhanad, Tugaleva, Elena, Bergin, Margaret Lynn, Ray Guo, Lin-Rui
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2020
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7710993/
https://www.ncbi.nlm.nih.gov/pubmed/33305235
http://dx.doi.org/10.1016/j.cjco.2020.07.008
Descripción
Sumario:Pulmonary artery intimal sarcoma (PAIS) is a very rare tumour. The prevalence of PAIS is estimated to be between 0.001% and 0.003%, but this may be an underestimation because of potential misdiagnosis due to its similar presentation to that of pulmonary thromboembolism. The prognosis is very poor, with median overall survival between 11 and 18 months. We report a case of a 36-year-old man who presented to our cardiac surgery clinic reporting nonspecific symptoms and was found to have PAIS requiring surgical resection and adjuvant chemotherapy. We outline the radiologic features, pathologic characteristics, surgical approach, and chemotherapy treatment utilized.

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