Pulmonary Artery Intimal Sarcoma: A Deadly Diagnosis in Disguise

Pulmonary artery intimal sarcoma (PAIS) is a very rare tumour. The prevalence of PAIS is estimated to be between 0.001% and 0.003%, but this may be an underestimation because of potential misdiagnosis due to its similar presentation to that of pulmonary thromboembolism. The prognosis is very poor, w...

Descripción completa

Detalles Bibliográficos
Autores principales: Rabbani, Mohamad, Hafiz, Ahmed, Algadheeb, Muhanad, Tugaleva, Elena, Bergin, Margaret Lynn, Ray Guo, Lin-Rui
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2020
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7710993/
https://www.ncbi.nlm.nih.gov/pubmed/33305235
http://dx.doi.org/10.1016/j.cjco.2020.07.008
_version_ 1783618049847328768
author Rabbani, Mohamad
Hafiz, Ahmed
Algadheeb, Muhanad
Tugaleva, Elena
Bergin, Margaret Lynn
Ray Guo, Lin-Rui
author_facet Rabbani, Mohamad
Hafiz, Ahmed
Algadheeb, Muhanad
Tugaleva, Elena
Bergin, Margaret Lynn
Ray Guo, Lin-Rui
author_sort Rabbani, Mohamad
collection PubMed
description Pulmonary artery intimal sarcoma (PAIS) is a very rare tumour. The prevalence of PAIS is estimated to be between 0.001% and 0.003%, but this may be an underestimation because of potential misdiagnosis due to its similar presentation to that of pulmonary thromboembolism. The prognosis is very poor, with median overall survival between 11 and 18 months. We report a case of a 36-year-old man who presented to our cardiac surgery clinic reporting nonspecific symptoms and was found to have PAIS requiring surgical resection and adjuvant chemotherapy. We outline the radiologic features, pathologic characteristics, surgical approach, and chemotherapy treatment utilized.
format Online
Article
Text
id pubmed-7710993
institution National Center for Biotechnology Information
language English
publishDate 2020
publisher Elsevier
record_format MEDLINE/PubMed
spelling pubmed-77109932020-12-09 Pulmonary Artery Intimal Sarcoma: A Deadly Diagnosis in Disguise Rabbani, Mohamad Hafiz, Ahmed Algadheeb, Muhanad Tugaleva, Elena Bergin, Margaret Lynn Ray Guo, Lin-Rui CJC Open Case Report Pulmonary artery intimal sarcoma (PAIS) is a very rare tumour. The prevalence of PAIS is estimated to be between 0.001% and 0.003%, but this may be an underestimation because of potential misdiagnosis due to its similar presentation to that of pulmonary thromboembolism. The prognosis is very poor, with median overall survival between 11 and 18 months. We report a case of a 36-year-old man who presented to our cardiac surgery clinic reporting nonspecific symptoms and was found to have PAIS requiring surgical resection and adjuvant chemotherapy. We outline the radiologic features, pathologic characteristics, surgical approach, and chemotherapy treatment utilized. Elsevier 2020-07-17 /pmc/articles/PMC7710993/ /pubmed/33305235 http://dx.doi.org/10.1016/j.cjco.2020.07.008 Text en © 2020 Canadian Cardiovascular Society. Published by Elsevier Inc. http://creativecommons.org/licenses/by-nc-nd/4.0/ This is an open access article under the CC BY-NC-ND license (http://creativecommons.org/licenses/by-nc-nd/4.0/).
spellingShingle Case Report
Rabbani, Mohamad
Hafiz, Ahmed
Algadheeb, Muhanad
Tugaleva, Elena
Bergin, Margaret Lynn
Ray Guo, Lin-Rui
Pulmonary Artery Intimal Sarcoma: A Deadly Diagnosis in Disguise
title Pulmonary Artery Intimal Sarcoma: A Deadly Diagnosis in Disguise
title_full Pulmonary Artery Intimal Sarcoma: A Deadly Diagnosis in Disguise
title_fullStr Pulmonary Artery Intimal Sarcoma: A Deadly Diagnosis in Disguise
title_full_unstemmed Pulmonary Artery Intimal Sarcoma: A Deadly Diagnosis in Disguise
title_short Pulmonary Artery Intimal Sarcoma: A Deadly Diagnosis in Disguise
title_sort pulmonary artery intimal sarcoma: a deadly diagnosis in disguise
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7710993/
https://www.ncbi.nlm.nih.gov/pubmed/33305235
http://dx.doi.org/10.1016/j.cjco.2020.07.008
work_keys_str_mv AT rabbanimohamad pulmonaryarteryintimalsarcomaadeadlydiagnosisindisguise
AT hafizahmed pulmonaryarteryintimalsarcomaadeadlydiagnosisindisguise
AT algadheebmuhanad pulmonaryarteryintimalsarcomaadeadlydiagnosisindisguise
AT tugalevaelena pulmonaryarteryintimalsarcomaadeadlydiagnosisindisguise
AT berginmargaretlynn pulmonaryarteryintimalsarcomaadeadlydiagnosisindisguise
AT rayguolinrui pulmonaryarteryintimalsarcomaadeadlydiagnosisindisguise

Ejemplares similares