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Liver transplantation as a novel strategy for resolution of congenital afibrinogenemia in a pediatric patient

Fibrinogen replacement therapy is a treatment mainstay for patients with afibrinogenemia and significant bleeding. A male infant with congenital afibrinogenemia and several spontaneous hemarthroses commenced cryoprecipitate prophylaxis but developed severe urticarial reactions. He transitioned to a...

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Detalles Bibliográficos
Autores principales:	Corrales‐Medina, Fernando F., Miloh, Tamir, O’Farrell, Candelaria, Andrews, David M., Tekin, Akin, De Angulo, Guillermo
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	John Wiley and Sons Inc. 2020
Materias:	HAEMOSTASIS
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7756576/ https://www.ncbi.nlm.nih.gov/pubmed/32890454 http://dx.doi.org/10.1111/jth.15090

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