Extraskeletal myxoid chondrosarcoma: a case report with adjuvant intraoperative treatment

Extraskeletal myxoid chondrosarcoma is a rare form of malignant mesenchymal neoplasm mainly localized into the limbs, particularly in the thigh and popliteal fossa. It has been classified as a low-grade sarcoma so far, but it shows a tendency to relapse and metastasize. In the early stage of disease...

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Autores principales: Bacchetti, Stefano, Pegolo, Enrico, Adani, Gianluigi, Macrì, Antonio, Andreetta, Claudia, Ermacora, Paola, Girometti, Rossano, Trovò, Marco, Driul, Lorenza, Di Loreto, Carla, Pasqual, Enricomaria
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Oxford University Press 2020
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7769219/
https://www.ncbi.nlm.nih.gov/pubmed/33391642
http://dx.doi.org/10.1093/jscr/rjaa503
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author Bacchetti, Stefano
Pegolo, Enrico
Adani, Gianluigi
Macrì, Antonio
Andreetta, Claudia
Ermacora, Paola
Girometti, Rossano
Trovò, Marco
Driul, Lorenza
Di Loreto, Carla
Pasqual, Enricomaria
author_facet Bacchetti, Stefano
Pegolo, Enrico
Adani, Gianluigi
Macrì, Antonio
Andreetta, Claudia
Ermacora, Paola
Girometti, Rossano
Trovò, Marco
Driul, Lorenza
Di Loreto, Carla
Pasqual, Enricomaria
author_sort Bacchetti, Stefano
collection PubMed
description Extraskeletal myxoid chondrosarcoma is a rare form of malignant mesenchymal neoplasm mainly localized into the limbs, particularly in the thigh and popliteal fossa. It has been classified as a low-grade sarcoma so far, but it shows a tendency to relapse and metastasize. In the early stage of disease, surgery represents the only chance of cure. In case of diffuse metastatic disease, systemic chemotherapy with anthracyclines is the standard of care. In this paper, we present a case of a patient affected by this rare disease and the analysis of radiological, surgical and histopathological aspects.
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spelling pubmed-77692192020-12-31 Extraskeletal myxoid chondrosarcoma: a case report with adjuvant intraoperative treatment Bacchetti, Stefano Pegolo, Enrico Adani, Gianluigi Macrì, Antonio Andreetta, Claudia Ermacora, Paola Girometti, Rossano Trovò, Marco Driul, Lorenza Di Loreto, Carla Pasqual, Enricomaria J Surg Case Rep Case Report Extraskeletal myxoid chondrosarcoma is a rare form of malignant mesenchymal neoplasm mainly localized into the limbs, particularly in the thigh and popliteal fossa. It has been classified as a low-grade sarcoma so far, but it shows a tendency to relapse and metastasize. In the early stage of disease, surgery represents the only chance of cure. In case of diffuse metastatic disease, systemic chemotherapy with anthracyclines is the standard of care. In this paper, we present a case of a patient affected by this rare disease and the analysis of radiological, surgical and histopathological aspects. Oxford University Press 2020-12-28 /pmc/articles/PMC7769219/ /pubmed/33391642 http://dx.doi.org/10.1093/jscr/rjaa503 Text en Published by Oxford University Press and JSCR Publishing Ltd. © All rights reserved. The Author(s) 2020. http://creativecommons.org/licenses/by-nc/4.0/ This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/4.0/), which permits non-commercial re-use, distribution, and reproduction in any medium, provided the original work is properly cited. For commercial re-use, please contact journals.permissions@oup.com
spellingShingle Case Report
Bacchetti, Stefano
Pegolo, Enrico
Adani, Gianluigi
Macrì, Antonio
Andreetta, Claudia
Ermacora, Paola
Girometti, Rossano
Trovò, Marco
Driul, Lorenza
Di Loreto, Carla
Pasqual, Enricomaria
Extraskeletal myxoid chondrosarcoma: a case report with adjuvant intraoperative treatment
title Extraskeletal myxoid chondrosarcoma: a case report with adjuvant intraoperative treatment
title_full Extraskeletal myxoid chondrosarcoma: a case report with adjuvant intraoperative treatment
title_fullStr Extraskeletal myxoid chondrosarcoma: a case report with adjuvant intraoperative treatment
title_full_unstemmed Extraskeletal myxoid chondrosarcoma: a case report with adjuvant intraoperative treatment
title_short Extraskeletal myxoid chondrosarcoma: a case report with adjuvant intraoperative treatment
title_sort extraskeletal myxoid chondrosarcoma: a case report with adjuvant intraoperative treatment
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7769219/
https://www.ncbi.nlm.nih.gov/pubmed/33391642
http://dx.doi.org/10.1093/jscr/rjaa503
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