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Primary Partial Empty Sella presenting with Prepubertal Hypogonadotropic Hypogonadism: A Case Report

Primary partial empty sella occurs when less than 50% of an enlarged or deformed sella turcica is filled with cerebrospinal fluid in the setting of unidentified etiologic pathological conditions. Prepubertal hypogonadotropic hypogonadism presenting as its main manifestation is rare since its peak in...

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Detalles Bibliográficos
Autores principales: Matabang, Maria Angela, Sapang, Buena
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Journal of the ASEAN Federation of Endocrine Societies 2020
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7784113/
https://www.ncbi.nlm.nih.gov/pubmed/33442193
http://dx.doi.org/10.15605/jafes.035.02.11
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author Matabang, Maria Angela
Sapang, Buena
author_facet Matabang, Maria Angela
Sapang, Buena
author_sort Matabang, Maria Angela
collection PubMed
description Primary partial empty sella occurs when less than 50% of an enlarged or deformed sella turcica is filled with cerebrospinal fluid in the setting of unidentified etiologic pathological conditions. Prepubertal hypogonadotropic hypogonadism presenting as its main manifestation is rare since its peak incidence commonly occurs late at 30 to 40 years of age and has a sexual predilection for female. We described a case of 20-year-old male who presented with micropenis and absent secondary sex characteristics. Work up showed cranial MRI finding of partial empty sella, low testosterone, LH, FSH, Estradiol and Beta HCG levels. Sex hormone replacement may not improve fertility for this case but may help produce and maintain virilization and prevent future complications of hypogonadotropic hypogonadism.
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spelling pubmed-77841132021-01-12 Primary Partial Empty Sella presenting with Prepubertal Hypogonadotropic Hypogonadism: A Case Report Matabang, Maria Angela Sapang, Buena J ASEAN Fed Endocr Soc Case Report Primary partial empty sella occurs when less than 50% of an enlarged or deformed sella turcica is filled with cerebrospinal fluid in the setting of unidentified etiologic pathological conditions. Prepubertal hypogonadotropic hypogonadism presenting as its main manifestation is rare since its peak incidence commonly occurs late at 30 to 40 years of age and has a sexual predilection for female. We described a case of 20-year-old male who presented with micropenis and absent secondary sex characteristics. Work up showed cranial MRI finding of partial empty sella, low testosterone, LH, FSH, Estradiol and Beta HCG levels. Sex hormone replacement may not improve fertility for this case but may help produce and maintain virilization and prevent future complications of hypogonadotropic hypogonadism. Journal of the ASEAN Federation of Endocrine Societies 2020-11-04 2020 /pmc/articles/PMC7784113/ /pubmed/33442193 http://dx.doi.org/10.15605/jafes.035.02.11 Text en © 2020 Journal of the ASEAN Federation of Endocrine Societies https://creativecommons.org/licenses/by-nc/4.0/ This work is licensed under a Creative Commons Attribution-NonCommercial 4.0 International.
spellingShingle Case Report
Matabang, Maria Angela
Sapang, Buena
Primary Partial Empty Sella presenting with Prepubertal Hypogonadotropic Hypogonadism: A Case Report
title Primary Partial Empty Sella presenting with Prepubertal Hypogonadotropic Hypogonadism: A Case Report
title_full Primary Partial Empty Sella presenting with Prepubertal Hypogonadotropic Hypogonadism: A Case Report
title_fullStr Primary Partial Empty Sella presenting with Prepubertal Hypogonadotropic Hypogonadism: A Case Report
title_full_unstemmed Primary Partial Empty Sella presenting with Prepubertal Hypogonadotropic Hypogonadism: A Case Report
title_short Primary Partial Empty Sella presenting with Prepubertal Hypogonadotropic Hypogonadism: A Case Report
title_sort primary partial empty sella presenting with prepubertal hypogonadotropic hypogonadism: a case report
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7784113/
https://www.ncbi.nlm.nih.gov/pubmed/33442193
http://dx.doi.org/10.15605/jafes.035.02.11
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