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Assessment of Adenosine Triphosphatase Phospholipid Transporting 8B1 (ATP8B1) Function in Patients With Cholestasis With ATP8B1 Deficiency by Using Peripheral Blood Monocyte‐Derived Macrophages
Adenosine triphosphatase phospholipid transporting 8B1 (ATP8B1) deficiency, an ultrarare autosomal recessive liver disease, includes severe and mild clinical forms, referred to as progressive familial intrahepatic cholestasis type 1 (PFIC1) and benign recurrent intrahepatic cholestasis type 1 (BRIC1...
Autores principales: | Mizutani, Ayumu, Sabu, Yusuke, Naoi, Sotaro, Ito, Shogo, Nakano, Satoshi, Minowa, Kei, Mizuochi, Tatsuki, Ito, Koichi, Abukawa, Daiki, Kaji, Shunsaku, Sasaki, Mika, Muroya, Koji, Azuma, Yoshihiro, Watanabe, Satoshi, Oya, Yuki, Inomata, Yukihiro, Fukuda, Akinari, Kasahara, Mureo, Inui, Ayano, Takikawa, Hajime, Kusuhara, Hiroyuki, Bessho, Kazuhiko, Suzuki, Mitsuyoshi, Togawa, Takao, Hayashi, Hisamitsu |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
John Wiley and Sons Inc.
2020
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7789840/ https://www.ncbi.nlm.nih.gov/pubmed/33437900 http://dx.doi.org/10.1002/hep4.1605 |
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