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Mitochondrial translation defects and human disease
In eukaryotic cells, mitochondria perform the essential function of producing cellular energy in the form of ATP via the oxidative phosphorylation system. This system is composed of 5 multimeric protein complexes of which 13 protein subunits are encoded by the mitochondrial genome: Complex I (7 subu...
Autores principales: | Webb, Bryn D., Diaz, George A., Prasun, Pankaj |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
2020
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7791537/ https://www.ncbi.nlm.nih.gov/pubmed/33426504 http://dx.doi.org/10.20517/jtgg.2020.11 |
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